2005
DOI: 10.2169/internalmedicine.44.177
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Hereditary Periodic Fever Syndromes in Japan

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Cited by 2 publications
(3 citation statements)
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“…This disease is concentrated in a particular area around the Mediterranean Sea and mostly seen among non‐Ashkenazi Jews, Armenians, Turks and Arabs (1:500–1:2000 prevalence). In Japan, so far at least nine families have been reported 9 . Skin rash, occurring specifically but less frequently compared with other major symptoms, resembles erysipelas and is histologically composed of massive neutrophil infiltration in dermis 10 .…”
Section: Hereditary Periodic Fever Syndromesmentioning
confidence: 99%
See 1 more Smart Citation
“…This disease is concentrated in a particular area around the Mediterranean Sea and mostly seen among non‐Ashkenazi Jews, Armenians, Turks and Arabs (1:500–1:2000 prevalence). In Japan, so far at least nine families have been reported 9 . Skin rash, occurring specifically but less frequently compared with other major symptoms, resembles erysipelas and is histologically composed of massive neutrophil infiltration in dermis 10 .…”
Section: Hereditary Periodic Fever Syndromesmentioning
confidence: 99%
“…In Japan, so far at least nine families have been reported. 9 Skin rash, occurring specifically but less frequently compared with other major symptoms, resembles erysipelas and is histologically composed of massive neutrophil infiltration in dermis. 10 Leukocytoclastic vasculitis such as polyarteritis nodosa (PN) and Henoch-Schonlein purpura (HSP) has also been reported to be associated with FMF.…”
Section: Hereditary Periodic Fever Syndromesmentioning
confidence: 99%
“…Although some reports indicated that E148Q was only one of the gene polymorphisms, other reports indicated that E148Q was associated with the mildest disease with a low penetrance or usually required another additional MEFV mutation to cause the classical manifestation of FMF [9,10]. Although FMF is an uncommon disorder in Japan, the frequency of E148Q is higher in Japanese than in European or Arab populations [11][12][13]. MEFV was predominantly expressed in granulocytes and monocytes [7], both of which play major roles in the pathophysiology of KD at the acute phase [2].…”
Section: Introductionmentioning
confidence: 99%