Herlyn-Werner-Wunderlich Syndrome Consisting of Uterine Didelphys, Obstructed Hemivagina and Ipsilateral Renal Agenesis in a Newborn

Wu, Tsung-Hsin; Wu, Trang-Tiau; Ng, Yan-Yan; Ng, Soo‐Cheen; Su, Pen‐Hua; Chen, Jia-Yuh; Chen, Suh-Jen

doi:10.1016/j.pedneo.2011.11.014

Cited by 61 publications

(68 citation statements)

References 10 publications

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“…Se produce alrededor de la novena semana de gestación, por un fallo en la fusión de los conductos de Müller verticales y laterales. Su etiología es desconocida y se caracteriza por la tríada de útero didelfo, hemivagina obstruida y agenesia renal unilateral 3 .…”

Section: Discussionunclassified

See 1 more Smart Citation

Síndrome de Herlyn-Werner-Wünderlich

Plans

Pons-Fuster

López

et al. 2015

Clínica e Investigación en Ginecología y Obstetricia

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Section: Discussionunclassified

“…Aunque la utilidad de esta técnica para el tratamiento quirúrgico no está clara, sí puede ayudar al drenaje del hematocolpos y/o al tratamiento de las complicaciones ya descritas 3,5 .…”

Section: Discussionunclassified

Síndrome de Herlyn-Werner-Wünderlich

Plans

Pons-Fuster

López

et al. 2015

Clínica e Investigación en Ginecología y Obstetricia

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“…Most patients present with non-specific postpubertal symptoms, generally from 2 to 12 months after menarche [19]. In a study including 70 patients with HWWS, Tong et al [1] reported a mean age at onset of symptoms of 17 years, ranging from 10 to 44.…”

Section: Clinical Presentationmentioning

confidence: 99%

“…So, the prepubertal diagnosis of the HWWS generally implies a high index of suspicion, which may come from prenatal or neonatal renal US. If renal agenesis is found in prenatal or neonatal US, particular attention should be provided to the external genitalia and, even in the absence of a pelvic or vulvar mass, the risk of further genital anomaly should be highlighted [19].…”

Section: Clinical Presentationmentioning

confidence: 99%

Herlyn–Werner–Wunderlich syndrome: pre- and post-surgical MRI and US findings

Dias

Jogo

2015

Abdom Imaging

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Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital anomaly of the female urogenital tract that associates Mu¨llerian duct anomalies with mesonephric duct anomalies. The triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis characterizes this syndrome. Patients generally present with non-specific symptoms after menarche. Pelvic pain, dysmenorrhea, and palpable mass due to hematocolpos or hematometra are the most common findings. Pyohematocolpos and pyosalpinx may appear as acute complications, while endometriosis and pelvic adhesions constitute potential long-term complications. When a prenatal diagnosis of unilateral renal agenesis in newborn girls is known, a gynecological imaging study should be performed to exclude uterine and vaginal abnormalities. These patients should be followed up to ensure that a timely surgical correction is performed. The diagnosis of HWWS is difficult due to the lack of specific symptoms or findings upon physical examination. An accurate imaging description of these congenital anomalies is crucial to guide patients toward surgical treatment, relieving acute complications, and preserving the normal fertility. The authors provide a pictorial review of the magnetic resonance imaging and ultrasonography findings of the HWWS with correlation to embryological, clinical, and surgical features.

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“…Fizik muayenede sağ tarafta daha sık olmak üzere tek taraflı pelvik kitle saptanır. 8 Ancak bizim olgumuz, sol obstrükte hemivajen ve sol hematokolposa bağlı pelvik kitle ile prezente olmuştur. Piyohematokolpos, piyosalpenks, piyoperitonit gibi enfektif süreçler, retrograd menstrüasyona sekonder endometriyoz ve pelvik adezyonlar karşılaşılabilecek komplikasyonlar arasındadır.…”

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