Herlyn-Werner-Wunderlich syndrome: Diagnosis and treatment of an atypical case and review of literature

Abstract

HighlightsIn this report we present a rare case of HWWS diagnosed in a 12-year-old female presenting with disabling abdominal pain after the onset of menarche.We reviewed patient’s clinical history, utility of diagnostic modalities, usual treatments, and recent literature.The purpose of this case report is to offer a better understanding of the pathophysiology of HWWS.When a young female presents with common, nonspecific symptoms, HWWS should be on differential diagnoses list.Greater awareness of HWWS will lead to earlier detection and, consequently, reduced complications caused by delayed diagnosis.

A Rare Case of Herlyn-Werner-Wünderlich Syndrome with an Ectopic Ureter and A Communication Between a Hydrocolpos and The Bladder Neck in A Uterus Didelphys

“…Cases of uterus didelphys with an obstructed hemivagina and kidney agenesia can present alongside other urinary tract malformations of the same side (OHVIRA) [6,7], an embryological alteration occurring in the 8th week of gestation [8].…”

Herlyn–Werner–Wunderlich syndrome and its complications: A report of two cases and literature review

“…The commonly used preoperative diagnostic methods for HWSS include ultrasound examination, hysterosalpingography, and MRI. CT imaging is not recommended for the screening and diagnosis of HWWS, as it is less accurate and subjects the patient to ionizing radiation [17] . Ultrasound examination is an inexpensive and convenient method of screening for HWWS; however, its diagnostic accuracy depends on the experience of the examiner.…”

Chronic pelvic pain caused by Herlyn-Werner-Wunderlich Syndrome: Case report and discussion

“…14However, Fauchin and al reported a case of hemiuterus with absent cervix where the vaginoplasty was not possible, the treatment was a laparoscopic hemi-hysterectomy with salpingectomy. (15) Rarely, hemi hysterectomy may be also considered in case of recurrent stenosis. 7Hysteroscopic resection of the septum under transabdominal guidance has also been reported in order to preserve the integrity of the hymen.…”