Histiocitose x (síndrome de hand-schuller-christian): relato de caso

Resumo: A his tio ci to se de célu las de Langerhans é repre sen tan te de um raro grupo de sín dro mes his tio citá rias, sendo carac te ri za da pela pro li fe ra ção das célu las de Langerhans. Suas mani fes ta ções variam de lesão soli tá ria a envol vi men to mul tis sis tê mi co, sendo o aco me ti men to vul var inco mum. Segue-se o rela to de caso refra tá rio da doen ça limi ta da à pele, em mulher de 57 anos. A pacien te apre sen ta va his tó ria de pápu las erite ma to sas ulce ra das em couro cabe lu do, face, vulva, tron co e axila há seis anos. O diag nós ti co da doen ça é difí cil, sendo con fir ma do neste caso atra vés de estu do imuno-his to quí mi co e se obte ve res pos ta tera pêu tica e efi caz, com a admi nis tra ção de tali do mi da. Palavras-chave: Histiocitose; Histiocitose de célu las de Langerhans; Histiócitos Abstract:Langerhans cell his tiocy to sis is a mem ber of a group of rare his tiocy tic syndro mes and is cha racte ri zed for the pro li fe ra tion of his tiocy tes cal led Langerhans'cells. Its mani fes ta tions vary from a soli tary injury to syste mic invol ve ment, and vul var lesions are uncom mon. We des cri be a refrac tory case of cutaneous limi ted disea se in a 57-year-old woman. She pre sen ted with a 6-year his tory of an ery the ma tous papu lar erup tion of the scalp, face, vulva, trunk and axil lae. The diag no sis is dif fi cult and in this case it was con fir med through immu no his to che mi cal study and cli ni cal impro ve ment was achie ved with tha li do mi de.

show abstract

Histiocitose de células de Langerhans com acometimento vulvar e com resposta terapêutica à talidomida: relato de caso

Fernandes

Guerra

Costa

et al. 2011

An. Bras. Dermatol.

View full text Add to dashboard Cite

show abstract

scite is a Brooklyn-based organization that helps researchers better discover and understand research articles through Smart Citations–citations that display the context of the citation and describe whether the article provides supporting or contrasting evidence. scite is used by students and researchers from around the world and is funded in part by the National Science Foundation and the National Institute on Drug Abuse of the National Institutes of Health.

Contact Info

customersupport@researchsolutions.com

10624 S. Eastern Ave., Ste. A-614

Henderson, NV 89052, USA

This site is protected by reCAPTCHA and the Google Privacy Policy and Terms of Service apply.

Blog Terms and Conditions API Terms Privacy Policy Contact Cookie Preferences Do Not Sell or Share My Personal Information

Made with 💙 for researchers

Part of the Research Solutions Family.

Histiocitose x (síndrome de hand-schuller-christian): relato de caso

Cited by 1 publication

References 10 publications

Histiocitose de células de Langerhans com acometimento vulvar e com resposta terapêutica à talidomida: relato de caso

Histiocitose de células de Langerhans com acometimento vulvar e com resposta terapêutica à talidomida: relato de caso

Contact Info

Product

Resources

About