Solitary eyelid neurofibroma is a rare condition, and there have been no reported cases of solitary eyelid neurofibroma involving the proximal lacrimal drainage system. A 6-year-old male presented with recurrent painless swelling in the medial part of the left lower eyelid. The patient was misdiagnosed as eyelid polyp and underwent excision biopsy twice elsewhere. Subsequently, the patient presented with a recurrence of swelling and was treated with full-thickness eyelid resection and reconstruction by direct closure. Histopathology showed the presence of spindle cells with hyperchromatic nuclei in a myxoid background. These cells showed S100 and CD 34 positivity. The systemic evaluation did not show any signs of neurofibromatosis.