Hybrid Palliation for Hypoplastic Left Heart Syndrome: Role of Echocardiography

Abstract

Hypoplastic left heart syndrome is a spectrum of complex congenital cardiac defects. Although in borderline cases, biventricular repair is a viable option, in the majority of cases, univentricular palliation is the treatment of choice. Hybrid palliation can be a valid alternative to classic Norwood operation in the neonatal period, especially in selected cases such as high-risk patients or borderline left ventricles. Echocardiography is the main diagnostic modality in this pediatric population, from the fetal diagnosis to the subsequent surgical steps of palliative treatment. Hybrid palliation is performed after birth and is characterized by surgical banding of the pulmonary arteries along with transcatheter stenting of the ductus arteriosus. There are some peculiar aspects of cardiac imaging that characterize this type of palliation, and that should be considered in the different phases before and after the procedure. We aimed to review the current literature about the role of echocardiography in the management of patients with hypoplastic left heart undergoing hybrid palliation.

Borderline Ventricles: From Evaluation to Treatment

“…There are also some experiences showing positive outcomes for delayed 2VR in borderline LV with mild hypoplasia after the neonatal hybrid palliation. In fact, this procedure may allow postponing the decision between single-ventricle palliation or 2VR until the LV has expressed its growth potential, usually after 4-6 months [44][45][46].…”