Hypoplasia and fibromuscular dysplasia of infrarenal abdominal aorta with downstream aneurysm: Case report and review of the literature

Abstract

Fibromuscular dysplasia represents one of the more common types of arterial fibrodysplasia, a heterogeneous group of nonatherosclerotic vascular occlusive and aneurysmal diseases. This disorder mainly affects renal and cerebral arteries, and less frequently, arm, leg, and visceral arteries. Exceptionally, it has been described in the abdominal aorta. Aortic hypoplasia is a tubular narrowing of a long segment of the aorta and is a rare congenital defect, different from coarctation, which is a focal stricture. We present the first case, to our knowledge, of an elderly man with infrarenal aortic fibromuscular dysplasia associated with aortic hypoplasia, without involvement of renal arteries, and contiguous aortoiliac aneurysm.

Hypereosinophilia and Multisite Vasculopathy of Fibromuscular Dysplasia: A Case Report

“…Odero et al reported a 77-year-old man with infrarenal aortic FMD and monoclonal gammopathy. 8) To the best of our knowledge, this is the first case report of FMD and hypereosinophilia. The association between the pathogenesis of these diseases is unclear, although the genetic abnormality may be assumed to be one of the important factors between these diseases.…”

Hypoplasia of Left Vertebral Artery with Intimal Fibromuscular Dysplasia in a Korean Woman

“…A few histologically confirmed cases are reported from intracranial vessels, but Kimura et al (6) only confirmed the medial hyperplasia type of FMD associated with aneurysm of the VA and posterior inferior cerebellar artery. Both hypoplasia and FMD in same vessel was only reported from abdominal aorta (7), but there was medial hyperplasia type of FMD associated with aneurysm. This is the first report consists of hypoplasia and intimal type FMD of the VA.…”

A case of fibro muscular dysplasia with abdominal aortic aneurysm

“…Most common presentations are renovascular hypertension and stroke. Fibro muscular dysplasia as a cause of abdominal aortic aneurysm is rather rarely reported [2,3,4]. Here we report a case of fibro muscular dysplasia associated with abdominal aortic aneurysm who presented with vague abdominal discomfort and claudication pain of both lower limbs.…”

“…Most common presentations are renovascular hypertension and stroke. Fibro muscular dysplasia as a cause of abdominal aortic aneurysm is rather rarely reported [2,3,4]. Clinical presentations of patients with FMD are varied.…”