“…The condition is also recognised as occurring infrequently in the UK although no published details of incidence are available. Indeed the disease is sufficiently uncommon outside Japan among Caucasians and Negroes that reports describe small numbers of cases or even single patients (Simon et al, 1968;Busch, 1969;Lepoire et al, 1969;Galligioni et al, 1971;O'Sullivan, 1973;Hoare and Keogh, 1974;Poor and Gacs, 1974;Sogaard and Jorgensen, 1975;Meriwether et al, H. B. Coakham, L. W. Duchen, and F. Scaravilli and symptoms of spatial disorientation, being unable to dress himself and losing his way in familiar surroundings. Over the previous four years he had developed progressive weakness of the proximal lower limb muscles, with symptoms including difficulty in rising from low chairs.…”