Hypoplastic left heart syndrome with anomalous origin of left coronary artery from the right pulmonary artery: successful surgical treatment in a neonate

Abstract

Anomalous origin of the left coronary artery from the right pulmonary artery in association with hypoplastic left heart syndrome is a rare congenital anomaly. We describe a successful simultaneous surgery for both anomalies during the first stage palliation in a neonate.

Pulmonary artery‐focused contrast echocardiography with supplemental oxygen(PCESO) for echocardiographic diagnosis of anomalous origin of left coronary artery from pulmonary artery: Novel use of an old technique

“…Among these, anomalous origin of LCA from the right pulmonary artery is extremely rare . Most reported cases of this type are associated with congenital heart diseases such as ventricular septal defect, aortopulmonary window, coarctation, hypoplastic left heart syndrome, and Shone's syndrome . However, our patient had no associated congenital heart disease.…”

“…10 Most reported cases of this type are associated with congenital heart diseases such as ventricular septal defect, aortopulmonary window, coarctation, hypoplastic left heart syndrome, and Shone's syndrome. [11][12][13][14][15] However, our patient had no associated congenital heart disease. Contrast echocardiography is an old technique with increasing applications.…”

Hypoplastic left heart syndrome with anomalous circumflex artery arising from left pulmonary artery. A description of combined surgical and interventional cardiac treatment

“…The first stage of HLHS treatment is a severe trauma for the child, and the surgery itself, as well as the duration of cardiopulmonary bypass, may be long [3]. Therefore, the probability of the patient developing coronary ischemia increases, especially in subjects with anomalies of the coronary arteries [4].…”

Anomalies of Left Coronary Artery Origin Affecting Surgical Repair of Hypoplastic Left Heart Syndrome and Shone Complex

“…The exact incidence of the association of these lesions with anomalous coronary arteries is unknown. The majority of reports involves case series or single case studies 1–16 . The most common coronary anomalies associated with left‐sided lesions consist of ventriculocoronary fistulas or coronary tortuosity; 14 anomalies of coronary origin are less common.…”

“…In our case, the coronary artery anomaly was clearly defined prospectively and allowed modification of surgical intervention to include coronary reimplantation, with an excellent result. There are few published case reports describing an abnormal origin of the left main 1–3 or circumflex 4,16 coronary artery from the RPA in patients with HLHS. There are additional case reports of anomalies such as the RCA 5 or a single coronary artery 6 arising from the pulmonary artery in HLHS.…”