A 51-year-old, right-handed, Caucasian, male factory mechanic with an underlying history of active tobacco abuse, hypertension and hyperlipidemia, awoke with severe, throbbing, left hand pain. His hand felt 'ice-cold'; 'like someone pulled my fingernails out'. He denied previous trauma of the involved upper limb or hand. He denied similar past symptomatology. Home medications included zolpidem, simvastatin, losartan, celecoxib, amitriptyline and diltiazem. His work activities were physically demanding, involving heavy use of his hands. He described a history of frequently using his left hand for pounding during previous employment as a farmer. For the previous 6 years, he had been employed as a factory mechanic, requiring less overall use of the left hand as a hammer, though he did still use this technique. Pounding activities using the right hand were much less frequent.He sought initial evaluation in the emergency department where Raynaud's phenomenon was suspected and a trial of cilostazol started. Symptoms, however, progressed to dusky, cyanotic-appearing 2nd, 3rd, 4th, and, to a lesser extent, 5th digits ( Figure 1) with worsening pain and hypersensitivity. Early signs of tissue loss were noted at the tip of the long finger (Figure 2
AbstractHypothenar hammer syndrome is an uncommon cause of upper-extremity ischemia that is often overlooked in the absence of a thorough occupational and recreational history. Importantly, it is a reversible cause of hand ischemia that, if missed, can lead to significant morbidity and even amputation. The occupational ramifications and quality of life of those affected can be significant. Its relative rarity, set against the ubiquitous use of the hand as a 'hammer' is noteworthy. Several other causes of hand ischemia can present similarly; therefore, consideration of other etiologies must be thoroughly investigated. Key distinguishing clinical features, in addition to a detailed occupational and recreational history, may include characteristic sparing of the thumb, the absence of a hyperemic phase in 'Raynaud's phenomenon', and a positive Allen's sign. Both non-invasive and invasive diagnostic studies, including bilateral upper-limb segmental pulse volume recordings (PVR), arterial duplex examination, and upper-extremity angiography, are complementary to a thorough history and physical examination. Optimal management strategies are not well defined because of its rarity and resultant lack of quality, evidence-based data. Though most cases can be successfully managed non-operatively, micrographic arterial reconstruction may be limb saving in severe or recalcitrant cases. Newer, experimental strategies including selective sympathetic blockage using botulinum toxin A have been reported in a few recalcitrant cases. The brief case description illustrates the typical presentation and potential treatment strategies employed in a difficult case. A review of relevant literature is also presented.