Gastrointestinal duplication cysts are rare lesions that typically present with acute abdomen in childhood. They are rare in adults, with only a few adult cases having been reported thus far. Adults with these lesions are usually asymptomatic or manifest with subtle abdominal symptoms. They may, however, also present with obstruction, bleeding, perforation, or malignancy. Herein, we aimed to report a case of ileal duplication cyst at adult age that presenting with symptoms of acute abdomen and reviewed the reported cases of adult age duplication cysts.