Iliac artery aneurysm in Marfan's Syndrome

Flanagan, Paul; Geoghegan, Justin; Egan, Timothy J.

doi:10.1016/s0950-821x(05)80217-8

Cited by 15 publications

(6 citation statements)

References 1 publication

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“…However, these aneurysms have been reported to occur in Marfan's syndrome and following pregnancy and infections. [8][9][10][11] Symptoms of iliac artery aneurysm occur either when it ruptures, producing abdominal pain, or as a result of direct compression of an adjacent structure in the pelvis.12 In our case, although the radiologic findings were suspicious for leaking aneurysm, the clinical presentation was more likely due to direct compression. Compression lumbosacral plexopathy, with unilateral lower limb numbness and weakness, and ureteric compression with hydronephrosis and hydroureter (asymptomatic) were the main clinical finding in our patient.…”

Section: Discussionmentioning

confidence: 71%

A Giant Isolated External Iliac Artery Aneurysm Causing Hydronephrosis and Lower Extremity Weakness

Wong¹,

Loftus

et al. 1999

Vascular Surgery

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A 75-year-old man was admitted with left lower limb weakness with findings of left isolated external iliac artery aneurysm and left hydronephrosis. Doppler ultrasound and contrasted computed tomography scan demonstrated a large 18 cm iliac artery aneurysm. Endoaneurysmorrhaphy and iliofemoral bypass were performed. The patient was well and discharged 2 weeks after operation. The incidence, natural history, and management of isolated iliac artery aneurysms are discussed and the literature is reviewed.

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Section: Discussionmentioning

confidence: 71%

A Giant Isolated External Iliac Artery Aneurysm Causing Hydronephrosis and Lower Extremity Weakness

Wong¹,

Loftus

et al. 1999

Vascular Surgery

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“…Recently, in addition to the well-characterized aortic abnormalities, there have been reports in MFS patients of aneurysm, dissection, dilatation, or rupture of the iliac, subclavian, carotid, uterine, and pulmonary arteries [8][9][10]. In contrast, renal involvement in MFS has been reported sporadically and has focused on structural abnormalities such as ectopia and duplex kidney [4].…”

Section: Discussionmentioning

confidence: 99%

Renovascular hypertension in Marfan syndrome

Baum

Harris

Burrows

et al. 1997

Pediatric Nephrology

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A defect in fibrillin integrity predisposes patients with Marfan syndrome to vascular wall abnormalities, most notably aortic rupture and dissection. Renal vascular anomalies have not been described previously in children with Marfan syndrome. In this report, we detail data from a hypertensive 14-year-old girl with clinical stigmata of Marfan syndrome and a diagnostic evaluation significant for characteristic aortic root dilatation and aneurysm, as well as a disparity in renal size and function exacerbated by captopril administration. Renal arteriography confirmed a left main renal artery stenosis that was not amendable to balloon angioplasty. Surgical resection resulted in significant improvement in hypertension. Pathological examination of the resected renal artery segment revealed intimal proliferation, fragmentation of the elastic media, and inner medial dissection. This patient demonstrates that, in addition to the aorta, renal arteries can be affected with the characteristic vascular wall pathology of Marfan syndrome, resulting in systemic hypertension. These data suggest that children with Marfan syndrome and hypertension need to be evaluated carefully for the presence of renal anomalies.

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“…Less well characterized are aneurysms and dissection of the peripheral vessels independent of aortic dissection. Isolated peripheral aneurysms have been described in Marfan syndrome in the carotid, subclavian, axillary, internal mammary, ulnar, iliac, and superficial femoral arteries [128][129][130][131][132][133][134][135][136][137][138]. A few studies have attempted to characterize the true prevalence of dilation or aneurysms in those without prior intervention.…”

Section: Aneurysm and Dissection Of Large-and Mediumsized Arteriesmentioning

confidence: 99%

Features of Marfan syndrome not listed in the Ghent nosology – the dark side of the disease

Kodolitsch

Demolder

Girdauskas

et al. 2019

Expert Review of Cardiovascular Therapy

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Introduction: The revised Ghent nosology presents the classical features of Marfan syndrome. However, behind its familiar face, Marfan syndrome hides less well-known features. Areas covered: The German Marfan Organization listed unusual symptoms and clinical experts reviewed the literature on clinical features of Marfan syndrome not listed in the Ghent nosology. Thereby we identified the following features: (1) bicuspid aortic valve, mitral valve prolapse, pulmonary valve prolapse, tricuspid valve prolapse, (2) heart failure and cardiomyopathy, (3) supraventricular arrhythmia, ventricular arrhythmia, and abnormal repolarization, (4) spontaneous coronary artery dissection, anomalous coronary arteries, and atherosclerotic coronary artery disease, tortuosity-, aneurysm-, and dissection of large and medium-sized arteries, (5) restrictive lung disease, parenchymal lung disease, and airway disorders, (6) obstructive-and central sleep apnea, (7) liver and kidney cysts, biliary tract disease, diaphragmatic hernia, and adiposity, (8) premature labor, and urinary incontinence, (9) myopathy, reduced bone mineral density, and craniofacial manifestations, (10) atrophic scars, (11) caries, and craniomandibular dysfunction, (12) headache from migraine and spontaneous cerebrospinal fluid leakage, (13) cognitive dysfunction, schizophrenia, depression, fatigue, and pain, (14) and activated fibrinolysis, thrombin, platelets, acquired von Willebrand disease, and platelet dysfunction. Expert commentary: Future research, nosologies, and guidelines may consider less well-known features of Marfan syndrome. ARTICLE HISTORY

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Iliac artery aneurysm in Marfan's Syndrome

Cited by 15 publications

References 1 publication

A Giant Isolated External Iliac Artery Aneurysm Causing Hydronephrosis and Lower Extremity Weakness

A Giant Isolated External Iliac Artery Aneurysm Causing Hydronephrosis and Lower Extremity Weakness

Renovascular hypertension in Marfan syndrome

Features of Marfan syndrome not listed in the Ghent nosology – the dark side of the disease

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