Imaging in osteofibrous dysplasia, osteofibrous dysplasia-like adamantinoma, and classic adamantinoma

Bethapudi, Sarath; Ritchie, D. A.; MacDuff, Elaine; Straiton, J.

doi:10.1016/j.crad.2013.09.011

Cited by 40 publications

(46 citation statements)

References 28 publications

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“…El gadolinio realza homogéneamente y de forma periférica en los quistes. 2,7 Sin embargo, estas características son poco específicas y también pueden corresponder a lesiones de etiología benigna (quiste óseo aneurismático, displasia fibrosa, displasia osteofibrosa). La displasia osteofibrosa es un tumor benigno que afecta principalmente la tibia en pacientes pediátricos (generalmente, menores de 10 años).…”

Section: Discussionunclassified

Adamantinoma en pediatría. Presentación de caso

et al. 2015

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Presentación de casos clínicos RESUMENEl adamantinoma es un tumor primario de los huesos largos, que afecta principalmente la diáfisis de la tibia, y es extremadamente raro en pediatría. Se presenta a partir de la segunda década de vida, con un ligero predominio en el sexo masculino. Se trata de un tumor de bajo grado, con alta agresividad a nivel local y bajo índice de metástasis y recurrencia una vez resecado en forma completa. Su diagnóstico resulta difícil, no solo por tratarse de una patología poco frecuente en pediatría, sino también por la dificultad para el diagnóstico diferencial con otras lesiones benignas. Presentamos el caso de un paciente de 15 años, con una tumoración indolora de larga evolución en la tibia distal, cuyo diagnóstico fue confirmado histológicamente con la pieza de amputación, ya que los estudios complementarios y las dos biopsias iniciales no fueron concluyentes. Aunque la mayoría de la bibliografía publicada consta de reportes de casos, y muy pocos en pacientes pediátricos, es de común acuerdo la dificultad para arribar al diagnóstico de adamantinoma. Palabras clave: adamantinoma, tumor óseo, tumor de bajo grado, pediatría.ABSTRACT Adamantinoma is a primary tumor of long bones, which affects mainly the shaft of the tibia, and is extremely rare in pediatrics. It frequently presents during the second decade of life, with a slight predominance in males. It is a low grade tumor, with local aggressiveness and low rate of metastasis and recurrence once it is completely removed. Its diagnosis is difficult, not only because it is a rare disease in children, but also because of the difficulty in the differential diagnosis with other benign lesions. We report the case of a 15-year-old patient with a painless swelling of the distal tibia, whose diagnosis was confirmed with the piece of amputation, as imaging features and both initial biopsies were not enough to achieve diagnosis. Though most of the literature consists of case reports, and very few in pediatric patients, they all agree on the difficulty in achieving the diagnosis of adamantinoma.

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Section: Discussionunclassified

Adamantinoma en pediatría. Presentación de caso

et al. 2015

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“…Pain and swelling are the most common presenting symptoms, and there is often a history of trauma [20,21].…”

Section: Adamantinomamentioning

confidence: 99%

“…Adamantinoma is a rare low-grade primary bone malignancy that most commonly occurs in the tibial diaphysis [20][21][22].…”

Section: Adamantinomamentioning

confidence: 99%

Surface primary bone tumors: Systematic approach and differential diagnosis

et al. 2015

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Surface primary bone tumors may appear similar to their intramedullary counterpart, but because they are rare, they may pose diagnostic challenges when showing different characteristics compared to their intramedullary counterpart. It is important for radiologists to recognize the imaging findings for various uncommon surface primary bone tumors, which may help to reduce the differential diagnosis or to lead to a specific diagnosis. Radiography is typically used for first-line imaging. If necessary, it is followed by CT or MRI for evaluation and characterization of surface bone tumors. The aim of this article is to review the imaging findings and differential diagnosis for surface primary bone tumors.

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“…The findings were consistent with those of cases previously reported in the literature, in that the skeletal angiomyolipoma may break through the bone cortex and invade adjacent soft tissues. The radiological differential diagnosis for angiomyolipoma of the skeleton includes chondroma, osteofibrous dysplasia and tuberculosis (11)(12)(13). Chondroma is associated with characteristic calcifications within the lesion.…”

Section: Discussionmentioning

confidence: 99%

Angiomyolipoma of the rib: A rare case report

Chen

Wang

Hu³

et al. 2015

Molecular and Clinical Oncology

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Abstract. Angiomyolipoma is a benign mesenchymal tumor, most commonly arising from the kidney. With the exception of the liver, extrarenal angiomyolipoma is an infrequent entity that may be misdiagnosed as other tumors. Angiomyolipoma occurring in the skeleton is an extremely rare occurrence and often difficult to differentiate from other bone diseases. We herein present a case of angiomyolipoma in the rib of a 44-year-old male patient, a highly unusual location for this type of tumor. Angiomyolipoma of the skeleton usually exhibits an infiltrative tendency. Although this clinical entity is rare, angiomyolipoma should be considered in the differential diagnosis of skeletal lesions, particularly in patients presenting with imaging findings of fat within the lesions.

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Imaging in osteofibrous dysplasia, osteofibrous dysplasia-like adamantinoma, and classic adamantinoma

Cited by 40 publications

References 28 publications

Adamantinoma en pediatría. Presentación de caso

Adamantinoma en pediatría. Presentación de caso

Surface primary bone tumors: Systematic approach and differential diagnosis

Angiomyolipoma of the rib: A rare case report

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