Incidental Diagnosis of Unicuspid Aortic Valve in an Asymptomatic Adult

Unicuspid Aortic Valve Presenting with Decompensated Critical Aortic Stenosis

“…This type of UAV has a pinhole-like orifice and is associated with neonatal hemodynamic compromise requiring urgent intervention. 7 …”

Unicuspid aortic valve in infant

“…The UAV is prone to be associated with dilatation or dissection of the aorta, involving the aortic root, ascending aorta, or aortic arch, which typically requires surgical intervention. [ 5 6 7 ] Other associated disorders include aortic coarctation, an aberrant right subclavian artery, and a single coronary artery and ventricular septal defects (VSDs). The importance of an early diagnosis of UAV lies in its risk of sudden cardiac death and association with other congenital anomalies, such as patent ductus arteriosus (PDA), VSD, anomalous coronary arteries, and coarctation of the aorta.…”

Severe Aortic Stenosis Associated with Unicommissural Unicuspid Aortic Valve in a Middle Aged Male

“…The later type of UAV has a relatively larger valve area, and symptoms present later in the forth to sixth decades of life. 1) 6) …”