Accessory chordae tendineae is an extremely rare anomaly. In this case report, we described a 61‐year‐old female patient newly diagnosed with the combination of an accessory mitral valve chordae extending from left atrium which is an extremely rare congenital anomaly and a bicuspid aortic valve. In our patient, three‐dimensional echocardiography showed incremental value over two‐dimensional echocardiography in the assessment of the exact localization and the extend of accessory chordea.