Incontinentia Pigmenti.

Lahiri, Kapil Deb

doi:10.1111/j.1365-2133.1955.tb12740.x

Cited by 7 publications

(4 citation statements)

References 7 publications

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“…[3] Cutaneous lesions may also be accompanied by defects of cutaneous appendages in the form of cicatricial alopecia or small and dystrophic nails. [4] Lesions may be seen either at birth or before the end of first week. Rarely, skin lesions start appearing after first 2 months of birth.…”

Section: Introductionmentioning

confidence: 99%

Case reports of incontinentia pigmenti in males

et al. 2013

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Incontinentia pigmenti is an X-linked dominant disorder, which is fatal in males, and majority of cases reported are in females. Here, we report 2 cases of males with incontinentia pigmenti. Case 1 has progressed through the classical stages of IP, giving history of vesicular and verrucous lesions and has presented with hyperpigmentation in whorled pattern. Case 2 has vesicular lesions in a linear distribution on the legs along with classical histopathological findings.

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Section: Introductionmentioning

confidence: 99%

Case reports of incontinentia pigmenti in males

et al. 2013

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“…As of eleven months of age we did not notice any systemic involvement in our patient. There are many reports of other systems involvement including cicatricial alopecia on the vertex 7 , nail dystrophy with onycholysis. 7,8 Roughly 30% of patients are found to have cicatricial alopecia, which may be the only remaining sign in an adult women.…”

Section: Fig-2: Visicles Following the Blascho's Linementioning

confidence: 99%

“…There are many reports of other systems involvement including cicatricial alopecia on the vertex 7 , nail dystrophy with onycholysis. 7,8 Roughly 30% of patients are found to have cicatricial alopecia, which may be the only remaining sign in an adult women. 9 Also reports of destructive encephalopathy 10 and retinopathy 11 are noted with bad prognosis.…”

Section: Fig-2: Visicles Following the Blascho's Linementioning

confidence: 99%

Incontinentia Pigmenti Involving Only the Skin

Wahiduzzaman

1970

J. Medicine

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Incontinentia pigmenti (IP) is an uncommon disorder which can affect the skin and other systems. . It is an X-linked dominant genodermatosis mainly affecting the female baby with prenatal lethality in boys. It was first reported by Garrod in 1906 and further defined by Bloch and Sulzberger in 1926 and 1928. It can involve the skin only or in addition can affect the central nervous system, eyes and the teeth. The boys do not survive unless associated with Klinefelter syndrome (47, XXY). Morbidity and mortality are related to neurologic and ophthalmologic sequelae. Our presented case did not have any systemic involvement but only cutaneous symptoms. doi:10.3329/jom.v10i1.2000 J Medicine 2009; 10: 25-27

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“…[6] reported in 1954 that the three clinical stages of the disease can present irregularly, each being of variable duration, and can even overlap occasionally. So far, three cases have been reported from India; by Lahiri [9] in 1955, M arquis and M ehta [11] in 1969, and R atan Singh and D evinder K au r [18] in 1970. C u r th and W a rburton [2] in 1965 discussed the heredofamilial nature of the disease and its occurrence only in females.…”

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Incontinentia Pigmenti et Achromians

Mittal¹,

Handa²,

Sharma³

1975

Dermatology

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A case is reported, apparently the first of its kind in the literature, of a female child in which there were not only pigmented lesions of incontinentia pigmenti but also hypopigmented lesions of incontinentia pigmenti achromians. The title incontinentia pigmenti et achromians is suggested for this combined disorder. The child also had associated lesions in the form of nail dystrophy, delayed dentition and epilepsy.

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Incontinentia Pigmenti.

Cited by 7 publications

References 7 publications

Case reports of incontinentia pigmenti in males

Case reports of incontinentia pigmenti in males

Incontinentia Pigmenti Involving Only the Skin

Incontinentia Pigmenti et Achromians

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