Inducible polymorphous ventricular tachycardia following Mustard operation for transposition of the great arteries

Abstract

A 22-year-old woman with chronic atrial tachycardia following Mustard's operation for transposition of the great arteries presented with dizziness and ventricular tachycardia documented with dynamic 24-h electrocardiogram. During intracardiac electrophysiology study, programmed ventricular extrastimulation induced polymorphous ventricular tachycardia (torsades de pointes). This was prevented by intravenous administration of procainamide. We postulate that polymorphous ventricular tachycardia is a possible cause of death in patients with Mustard's operation. Postoperative electrophysiologic study may define those patients at risk to develop this potentially fatal arrhythmia.

Predictors of sudden cardiac death after mustard or senning repair for transposition of the great arteries

“…Routine follow-up ECGs or 24-h Holter recordings showed few rhythm disturbances and were consequently of little help in identifying patients at risk. Scagliotti et al (31) postulated that inducible polymorphic VT at electrophysiology study may be a marker for SD and advocated the use of electrophysiology studies as risk-stratifying tests in these patients. No study to date has explored this hypothesis.…”

Status of survivors after atrial redirection for transposition of the great arteries: a complete long‐term follow‐up

“…The significance of inducible ventricular tachycardia in some Mustard patients (27) is unknown and one study failed to reveal any relationship between ventricular arrhythmias and sudden death (24). Ventricular dysfunction and tricuspid regurgitation are independent risk factors for sudden death (24) and, as atrial flutter further compromises ventricular function, these factors may potentiate one another (2 1, 24).…”