Infantile Bowel Obstruction in a Patient with Situs Inversus Totalis and Polysplenia: A Case Report

Abstract

The infantile intestinal obstruction associated with situs inversus totalis and polysplenia is extremely rare, with only a few cases reported in the literature. Furthermore, the management of this association is complicated. We report a case of a 2-month-old boy with intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine associated with situs inversus totalis, polysplenia, and pulmonary hypertension. To the best of our knowledge, this is the first case of situs inversus totalis with polysplenia, pulmonary hypertension, and intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine.

Polysplenia with situs inversus totalis, azygos continuation of the inferior vena cava, and duplication of the superior vena cava in a healthy adult: A case report

“…Our patient presented with anatomic features of both PS and SIT, which is exceedingly rare. Only 5 case reports have described a similar combination of findings [ [14] , [15] , [16] , [17] , [18] ]. His anatomic features in keeping with PS include multiple splenules, a shortened pancreas without a tail, azygos interruption of his inferior vena cava, and hepatic vein drainage into the right atrium.…”

“…These cardiovascular variants are benign and occur in the general population at frequencies of 0.4%-1.8%, 0.3%, and 3% respectively [ [19] , [20] , [21] ]. However, only case report described PS and SIT in the context of aortic arch branch variations [ 15 ], and the occurrence of the retroesophageal left subclavian artery and the duplicated superior vena cava has not yet been reported to occur in the context of PS and SIT.…”