“…It presents a condition similar to inflammatory pseudotumor, but more aggressive and with a worse response to steroids (8) . The diagnosis is obtained by exclusion.For that, the medical history, clinical examination, laboratory tests for differential diagnosis with other diseases (T3, T4, TSH, VHS, glucose, urea, creatinine, blood cultures), CT scan, biopsy and treatment response are evaluated (9) . Systemic corticosteroids are the first line of treatment for orbital pseudotumors, usually starting with a dose of 1 to 2 mg/kg/ day of oral prednisone (2) .…”