Intestinal lymphangiectasia — a report of two cases

Abstract

Intestinal lymphangiectasia is a rare benign disease characterised by focal or diffuse dilation of the mucosal, submucosal and subserosal lymphatics. Clinically, the patients may present with protein losing enteropathy (PLE), hypoproteinemic oedema, chylous ascites, pleural effusion, acute appendicitis and intestinal obstruction.

Primary intestinal lymphangiectasia: Multiple detector computed tomography findings after direct lymphangiography

“…Early diagnosis and treatment of PIL is of great importance for effective diet therapy. Small bowel resection is useful in some patients with segmental and localized intestinal lymphangiectasia . In our study, intra‐ and extraintestinal abnormalities, especially with regard to morphology and extent of lymphatic vessel involvement can be observed, providing valuable clue to the diagnosis of PIL and the determination of a treatment strategy.…”

“…Intestinal lymphangiectasia (IL) is an uncommon protein‐losing gastroenteropathy caused by congenital malformation or obstruction of intestinal lymphatic drainage, and is associated with extraintestinal lymphatic abnormalities . IL is categorized into two types based upon its aetiology: primary intestinal lymphangiectasia (PIL) and secondary intestinal lymphangiectasia (SIL) .…”

“…PIL usually occurs in children and adolescents due to the congenital deformity of the small bowel lymphatic system, whereas SIL is more often seen in adults and occurs secondary to elevated lymphatic pressure caused by lymphoma, constrictive pericarditis, inflammatory bowel disease, malignancies, systemic lupus erythematosus or cardiac surgery . Given its rare nature, most publications to date have been isolated case reports . Although individual case reports of the CT findings of PIL have been published, to the best of our knowledge, no descriptions of MDCT findings after direct lymphangiography in PIL exist.…”

“…Intestinal lymphangiectasia (IL) is an uncommon protein-losing gastroenteropathy caused by congenital malformation or obstruction of intestinal lymphatic drainage, and is associated with extraintestinal lymphatic abnormalities. 1,2 IL is categorized into two types based upon its aetiology: primary intestinal lymphangiectasia (PIL) and secondary intestinal lymphangiectasia (SIL). [3][4][5] PIL usually occurs in children and adolescents due to the congenital deformity of the small bowel lymphatic system, whereas SIL is more often seen in adults and occurs secondary to elevated lymphatic pressure caused by lymphoma, constrictive pericarditis, inflammatory bowel disease, malignancies, systemic lupus erythematosus or cardiac surgery.…”

An unusual case of chylous ascites: A case report

“…Some patients have a short period of fever initially, while others present with acute ileus and some develop the symptoms gradually [2,4,5,[8][9][10][11][12][13][14][15] .…”