Intra-Peritoneal Leiomyoma of the Round Ligament in a Patient with Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome

G, Salem Wehbe; Bitar, Roger; Zreik, Tony G.

doi:10.21767/2471-8165.1000038

Cited by 3 publications

(6 citation statements)

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“…We should keep in mind that she has normal functioning ovaries and fallopian tubes, there is a chance for getting the child from the surrogate technique by retrieving the ovum [ 6 ]. Uterine remnants could present in varying sizes, consist of fibromuscular tissue, a small number of smooth muscles (myometrium), and stroma tissue arranging in glands (endometrium).…”

Section: Clinical Discussionmentioning

confidence: 99%

A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach

Harzif

Ambalagen

Charilda

et al. 2021

International Journal of Surgery Case Reports

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Section: Clinical Discussionmentioning

confidence: 99%

A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach

Harzif

Ambalagen

Charilda

et al. 2021

International Journal of Surgery Case Reports

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“…4,8 In order to make a definitive diagnosis, a clinical examination followed by pelvic ultrasonogram and MRI, and karyotype are required. [1][2][3][4]8 For many patients, the initial presentation is normal female sexual characteristics with primary amenorrhea. According to medical literature, there are many causes of amenorrhea and MRKH syndrome is the second most common cause.…”

Section: Discussionmentioning

confidence: 99%

“…According to medical literature, there are many causes of amenorrhea and MRKH syndrome is the second most common cause. 4,8,9 This syndrome has gone through multiple revisions in its description to capture the entire picture between 1829 and 1961. In 1829, Mayer described various vaginal anomalies not limited to duplications because of abnormal development of the Mullerian ducts.…”

Section: Discussionmentioning

confidence: 99%

“… 1 , 3 Secondary sexual characteristics are present with a 46 XX karyotype. 4 , 8 In order to make a definitive diagnosis, a clinical examination followed by pelvic ultrasonogram and MRI, and karyotype are required. 1 - 4 , 8 For many patients, the initial presentation is normal female sexual characteristics with primary amenorrhea.…”

Section: Discussionmentioning

confidence: 99%

“…According to medical literature, there are many causes of amenorrhea and MRKH syndrome is the second most common cause. 4 , 8 , 9 …”

Section: Discussionmentioning

confidence: 99%

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Incidental Finding of Leiomyoma in Mayer-Rokitansky-Kuster-Hauser Syndrome

Ibidapo-Obe

Okudo

Filani

2021

Journal of Investigative Medicine High Impact Case Reports

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Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a sexual developmental disorder. In this disorder, there is a congenital absence of the uterus and vagina with normal external genitalia. The etiology is not well understood. Variations of this condition exist that may include congenital abnormalities and psychological problems. In this article, we discuss the case of a 47-year-old African American female who presented with acute renal failure, solitary right kidney, and a pelvic mass extending from the pelvis to the right hypochondrium determined to be a fibroid. The patient was managed by a multidisciplinary team, dialyzed, and planned for removal of the mass. While understanding the low probability of having fibroids without a uterus, fibroids should not be excluded from such patients. It is also important to consider the emotional and psychological well-being of such patients.

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Rare case of bizarre leiomyoma in Mayer-Rokitansky-Küster-Hauser Syndrome

Sun,

Wang,

et al. 2020

Clin. Exp. Obstet. Gynecol.

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The authors report a case of leiomyoma that developed from an aplastic uterus in a 38-year-old Chinese female with a typical Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome. She had normal female secondary sexual characteristics, normal external genitalia with discernible vagina, primary amenorrhea, and infertility with asymptomatic a left adnexal mass. Pelvic MRI showed a mass of 3.7 cm in the left pelvis and a mass of 1.5 × 1.4 × 2.6 cm 3 in the right pelvis without a normal functioning uterus and vagina between the bladder and rectum. Laparoscopic exploration showed that the bilateral rudimentary uteri located laterally in the pelvis and they had a constant caudal relationship with their paired ovary. The bilateral fallopian tubes and ovaries were normal. A leiomyoma developed from the left rudimentary uteri. Removal of the left leiomyoma, bilateral rudimentary uteri and fallopian tubes was performed with preservation of bilateral ovaries. The histologic diagnosis showed that the bilateral rudimentary uteri had no clear structures of uterine cavity and endometrium, and the bizarre leiomyoma developed from the left rudimentary uterus without necrosis or mitosis.

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Intra-Peritoneal Leiomyoma of the Round Ligament in a Patient with Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome

Abstract: Background: The occurrence of an extra-uterine leiomyoma, arising from the intra-peritoneal portion of the round ligament in a lady with Müllerian agenesis diagnosed at the age of forty is extremely rare. We report a case of this rare combination in a Middle Eastern woman.

Cited by 3 publications

References 4 publications

A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach

A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach

Incidental Finding of Leiomyoma in Mayer-Rokitansky-Kuster-Hauser Syndrome

Rare case of bizarre leiomyoma in Mayer-Rokitansky-Küster-Hauser Syndrome

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