A 64‐year‐old man presented with back pain and dysesthesia in the arms. Neurological examination results were unremarkable. T2‐weighted MRI revealed an abnormal intensity mimicking myelitis with longitudinally extensive spinal cord lesions. Contrast‐enhanced T1‐weighted MRI revealed an enhanced intramedullary mass at the Th7 level. CSF showed slight pleocytosis and elevated protein levels. CT and PET of the whole body showed no significant findings. The lesion was removed surgically and was compatible with capillary hemangioma histologically. Postoperatively, his symptoms and the long cord lesion were resolved. This case indicates that marked edema mimicking myelitis can be caused by intramedullary capillary hemangioma.