In this review, clinical findings, diagnosis, and treatments of pediatric mass lesions of the fundus were summarized which are seen less often. Idiopathic choroidal granuloma, medulloepithelioma, juvenile xanthogranuloma, fibrous histiocytoma, intraocular teratoma, and ophthalmic findings of Klippel–Trenaunay–Weber syndrome were summarized. These lesions should be kept in the mind for differential diagnosis during ocular oncology practice.