Facial nerve schwannoma is an uncommon benign tumor, which is rarely encountered in the parotid gland, and mimicking the tumors of this gland. It's a neurogenic lesion that arises from Schwann cells of peripheral nerve sheath. Most of cases, it is localized in the intratemporal segment of the facial nerve, only 9% that occur in the extratemporal segment. Intraparotid facial nerve schwannoma was firstly described by Ibarz in 1927. Even if the tumor arises from the nerve itself, the function of the facial nerve is generally unaffected. If there is facial paralysis, it is interfered with malignant parotid tumors. Because of the heterogeneity of imaging features, it is difficult to diagnosis and differentiate preoperatively the intraparotid facial nerve schwannoma from other parotid tumors, so the definitive diagnosis is made by histological examination of resected tumor. The management of intraparotid facial nerve schwannoma is a very contested issue within the literature. Because the benignity and low evolutionary potential of the tumor, some authors advocating a conservative attitude with clinical surveillance for patients without facial nerve dysfunction or for tumor localized in the parotid gland. However, if a severe or a sudden facial nerve dysfunction, or extension into the mastoid was founded, the surgical resection of the tumor is indicated without delay. We report a case of a 24-year-old young female, complaining of a slow-growing and painless mass in the left parotid area, associated with grade V facial paralysis on left side since 10 years. No lymphadenopathy was founded in the neck. The computed tomography scan was revealed a heterogeneous tumor, involving in superficial and deep lobes of the left parotid gland, and extending into the parapharyngeal space. On surgical exploration, the dissection of facial nerve and isolation of the mass was impossible. Because the patient had a facial paralysis preoperatively, we had to sacrifice the facial nerve to remove the tumor by total parotidectomy for definitive diagnosis and treatment. The tumor was histopathologically confirmed to be schwannoma of facial nerve in the left parotid gland. The purpose of this study is to highlight the rarity of intra-parotid facial nerve schwannoma occurrence, its clinical features, and the difficulties of diagnosis and management, with review of the literature.