Intrapelvic Retroperitoneal Synovial Sarcoma in a 15-Year-Old Adolescent Girl: A Case Report and Review of the Literature

Bessems, Stan A.M.; Heinsbergen, Maarten van; Nijhuis, P.H.A.; Ven, Kees C P van de; Aarts, Frits

doi:10.1097/mph.0000000000001583

Cited by 3 publications

(2 citation statements)

References 15 publications

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“…We suggest follow-up each quarterly for 5 years, especially in high-risk cases, that precocious late metastasis is reported [20].…”

Section: Discussionmentioning

confidence: 90%

Children Kidney Synovial Sarcoma (KSS): A case report and literature reviewed from National Cancer institute-Brazil/RJ

Carvalho,

Martins,

Macedo

et al. 2024

Preprint

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We report an uncommon presentation of kidney synovial sarcoma (KSS) in childhood, discovered by abdominal pain and gross hematuria, associated to radiological and pathological challenges to the diagnosis. After necessary biopsy, adequate chemotherapy, following European Pediatric Soft Tissue Sarcoma Study Group Non-Rhabdomyosarcoma NRSTS 2005 Protocol, completely resection was possible. There are just few cases at global literature review of SSR in child, a good response to treatment is performed a completely resection (R0), besides a close follow-up (strongly recommended). The risk of metastasis is strongly correlated that is why diagnosis represent a big deal.

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“…We suggest follow-up each quarterly for 5 years, especially in high-risk cases, that precocious late metastasis is reported [20].…”

Section: Discussionmentioning

confidence: 90%

Children Kidney Synovial Sarcoma (KSS): A case report and literature reviewed from National Cancer institute-Brazil/RJ

Carvalho,

Martins,

Macedo

et al. 2024

Preprint

View full text Add to dashboard Cite

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“…The most common site is the extremities near the large joints (70%). 1 Primary pelvic synovial sarcoma is exceptionally rare; only a few cases have been reported in the literature, [2][3][4][5][6][7][8][9][10][11][12] and we could not determine the exact incidence. Histologically, synovial sarcoma has 2 main subtypes: (1) biphasic with both epithelial and spindle cell components, and (2) monophasic with predominantly spindle cells.…”

Section: Introductionmentioning

confidence: 99%

Pelvic Synovial Sarcoma Clinically Masquerading as an Ovarian Malignancy

Gupta

Nalwa

Vedant

et al. 2022

TOJ

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Background: Synovial sarcoma, a malignant mesenchymal tumor, commonly involves the extremities and is rarely found in the pelvis. Cytology with a biphasic pattern can suggest the diagnosis of synovial sarcoma. Case Report: A 32-year-old female presented with complaints of abdominal distension. She was initially evaluated in another hospital where she underwent ultrasound-guided fine needle aspiration cytology (FNAC) of the abdominal mass. The mass was diagnosed as ovarian adenocarcinoma, and the patient underwent 3 cycles of chemotherapy. After 3 months, she was referred to our institute for surgical excision of the mass. Contrast-enhanced computed tomography of the abdomen suggested a wellcircumscribed, heterogeneous, solid-cystic mass in the left adnexal region measuring 13.9 × 10 × 9.1 cm and compressing the adjacent structures. No previous radiologic investigations were available. We reviewed the FNAC slide from the outside hospital and made a preliminary diagnosis of biphasic synovial sarcoma. The patient underwent debulking surgery consisting of panhysterectomy with excision of the pelvic mass. Microscopic examination of the pelvic mass showed a biphasic tumor composed of epithelial and mesenchymal components, suggestive of synovial sarcoma. The immunohistochemistry profile supported the morphologic diagnosis. Bilateral ovaries were unremarkable. The patient received 4 cycles of adjuvant chemotherapy and is presently asymptomatic. Conclusion: Although primary pelvic synovial sarcoma is a rare occurrence, this case illustrates that synovial sarcoma can be diagnosed or at least suspected on FNAC. Because of the importance of adjuvant chemotherapy, synovial sarcoma must be high on the list of differential diagnoses of high-grade intra-abdominal masses.

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SS18-SSX Translocation FISH Negative Mesenteric Synovial Sarcoma-Documentation of an Extremely Rare Entity

Mathew

Sleeba

Subi

et al. 2020

J Gastrointest Canc

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Intrapelvic Retroperitoneal Synovial Sarcoma in a 15-Year-Old Adolescent Girl: A Case Report and Review of the Literature

Cited by 3 publications

References 15 publications

Children Kidney Synovial Sarcoma (KSS): A case report and literature reviewed from National Cancer institute-Brazil/RJ

Children Kidney Synovial Sarcoma (KSS): A case report and literature reviewed from National Cancer institute-Brazil/RJ

Pelvic Synovial Sarcoma Clinically Masquerading as an Ovarian Malignancy

SS18-SSX Translocation FISH Negative Mesenteric Synovial Sarcoma-Documentation of an Extremely Rare Entity

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