Intrapulmonary artery septation for unilateral absence of the pulmonary artery

Abstract

We describe a seven-month-old boy with tetralogy of Fallot and an absent left pulmonary artery. Due to the diminutive size of the left pulmonary artery, we performed a native tissue left pulmonary artery reconstruction and intrapulmonary artery septation procedure with a left modified Blalock-Taussig shunt. After confirming left pulmonary artery growth, the patient underwent tetralogy of Fallot repair, removal of septation patch, and division of the Blalock-Taussig shunt. Nine months post-surgery, we confirmed his balanced lung perfusion (R/L ratio 6:4). The intrapulmonary artery septation procedure would be suitable for both the resuscitation and reconstruction of the hypoplastic absent pulmonary artery.

Pulmonary artery reconstruction and correction of tetralogy of Fallot combined with the absence of the mediastinal left pulmonary artery

“…However, if the LPA can be effectively reconstructed, one-stage bilateral pulmonary artery TOF repair can be achieved.Due to the length of the lacking segment and few available blood vessel tissue, reconstruction of the connection between the LPA and the main pulmonary artery is a challenge for surgeons. Various techniques and reconstructive materials have been reported [9][10][11][12][13]. In our institute, different surgeons have different techniques and strategies.…”