Intrathoracic desmoid tumor with invasion of the great vessels

Abstract

A desmoid tumor of the mediastinum was diagnosed and treated in a 35-year-old white male who presented with a right supraclavicular mass. He was treated with resection, which involved several vascular structures, requiring multiple vascular reconstructions followed by post-operative radiotherapy. The authors concluded that, when located in the mediastinum, the invasive character of such tumors and its tendency to recur may pose a considerable surgical challenge, requiring careful pre-operative planning and long term post-operative follow -up. The role of radiation therapy is limited to the control of local recurrences.

Bilateral Breast Fibromatosis: Case Report and Review of the Literature

“…42 When surgical excision is not appropriate or achievable in selected patients, or whenever surgery with positive margins was performed, radiotherapy has been used. 43 Either associated with surgery or used alone (50-60 Gy), radiotherapy achieves a longstanding control in 70% to 80% of patients. A higher dose level may lead to an increase in complications.…”

Desmoid Tumor of the Facet Joint: A Case Report

“…In cases of limited surgery and radical resection of the tumor tissue, local irradiation is recommended5,13). The role of radiation therapy in an adjuvant setting, if any, is limited to the control of local recurrences3). The role of adjuvant radiotherapy in patients with positive margins following resection of the primary disease is controversial, and should be based on potential morbidity from radiotherapy compared to the potential morbidity of another local recurrence.…”

“…The role of adjuvant radiotherapy in patients with positive margins following resection of the primary disease is controversial, and should be based on potential morbidity from radiotherapy compared to the potential morbidity of another local recurrence. Some data suggest that postoperative radiation with 50-60Gy may improve progression-free survival in incompletely excised tumors with acceptable morbidity3,10,12). The effectiveness of chemotherapy and hormone therapy could not be verified; thus, both are used as alternatives in those cases in which adequate local treatment cannot be done15).…”

Trudności w Diagnostyce i Leczeniu Włókniakowatości śródpiersia. Opis Przypadku

“…Powstawaniu tego nowotworu mogą sprzyjać urazy (też operacyjne), czynniki hormonalne (głównie estrogeny), ciąża. Guzy te mogą zajmować różne obszary anatomiczne, najczęściej obręcz barkową, ścianę klatki piersiowej, okolicę okołokręgosłupową, udo [2,3]. W 20% przypadków lokalizacja jest w ścianie klatki piersiowej, natomiast rzadko występują wewnątrz niej [2,4].…”

“…Guzy tego typu mogą przebiegać bezobjawowo i są rozpoznawane przypadkowo [2,5]. Często wywołują jednak objawy powodowane uciskiem albo naciekaniem otaczających struktur, na przykład ucisk na nerwy wywołujący ból, na przełyk -dysfagię, czy na drogi oddechowe będący przyczyną duszności albo niewydolności oddechowej [3,4,8]. Fibromatoza nie daje przerzutów odległych i nie ma cytologicznych cech złośliwości.…”