Intrathoracic lipoblastoma in a 8 month old infant

Mollaian, Mansour; Shahgholi, E; Ghodsi, Maryam; Oskuoei, Ayda Khabazi

doi:10.1016/j.epsc.2020.101429

Cited by 1 publication

(2 citation statements)

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“…LB vary widely in anatomical location. The most affected regions reported are the subcutaneous tissue of the trunk and limbs (3), but intrathoracic, intraabdominal, head, neck, axillary, inguinal or genital localizations are occasionally described in the literature (1)(2)(3)(4)(5)(6)(7)(8)(9)(10)(11). They usually present as a solitary soft palpable mass, usually painless (3,5).…”

Section: Introductionmentioning

confidence: 99%

“…The cosmetic aspects, the mass effect or the broad spectrum of the localization of the LB (some of them requiring a cautious attitude) can influence the surgeon's decision. Histopathologic examination along with immunohistochemistry is the standard of definitive diagnosis, while complete surgical excision is the current mainstay treatment ( 2 , 9 , 11 , 12 ).…”

Section: Introductionmentioning

confidence: 99%

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Lipoblastoma: Diagnosis and surgical considerations

et al. 2021

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Lipoblastoma (LB) and lipoblastomatosis (LBS) are uncommon benign mesenchymal tumors of embryonal fat, occurring almost exclusively in infancy and early childhood. These fast-growing tumors have an excellent prognosis if properly treated. Eight consecutive children having pathologically demonstrated LB treated by the same surgical team were retrospectively reviewed. There were 5 boys and 3 girls between 7 to 36 months (median age 22 months). The localization of the tumors was on the thigh (1 case), abdomen (2 cases), axillary and pectoral region (1 case) paragluteal region (1 case), lumbar area (1 case), inguinal-scrotal (1 case), and in one case, presacral, gluteal and perirectal region (1 case). Five were focal and in 3 cases an infiltrative growth pattern was observed. One case exhibited a gross appearance resembling sacrococcygeal teratoma, with associated Dravet syndrome. No recurrence was noted in our series, after a mean follow-up of 28 months post operatory. Despite its rareness, LB must be kept in mind when diagnosing a rapidly growing fatty mass in children. Even when dealing with very large abdominal LB, complete surgical excision is possible, with an excellent prognosis. Due to the relatively high recurrence rate noted in the literature, particularly in LBS, follow-up is extremely important.

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