Involvement of the incudostapedial joint anomaly in conductive deafness

Abstract

Fifteen cases of ossicular anomalies without external ear malformation were studied. The anomaly of the incus-stapes complex was the most frequent. There were two cases of fused incudostapedial (IS) joint, which is an extremely rare occurrence. Case 1 was a 33-year-old man, in whom otosclerosis was suspected and exploratory tympanotomy was performed. The IS joint was fused, and the stapes was immobile. Small fenestra stapedectomy was performed. In case 2, a 52-year-old woman, otosclerosis was also suspected and exploratory tympanotomy was performed. The IS joint was fused and the incus was fixed. After the long process of the incus was cut, the stapes became mobile. However, since the incus remained immobile, it was removed and was placed on the stapes. In both cases, the hearing improved after surgery. The averaged hearing gain of 15 cases was 28.8 dB.

Prolyl 3-hydroxylase-1 null mice exhibit hearing impairment and abnormal morphology of the middle ear bone joints

“…Incudostapedial joint dislocation and stapes fixation are the most common anomalies among ossicular malformations (Suzuki et al, 2008). We took a closer look at the middle ear bones in the P3H1 null mice.…”

Reporting and Description for Congenital Middle Ear Malformations to Facilitate Surgical Management

“…Table 3 lists the detailed ossicular chain reconstruction of type Ia (113 cases) in the articles. [6][7][8][9][10][11][12][13][14][15][16][17][18][19][20] The percentages of patients with deformities in the stapes suprastructure, incus, and malleus were 50.9%, 48.0%, and 18.3%, respectively. Aberrant facial nerves were found in 14 type II patients and 129 type III patients.…”

“…In the present study, our retrospective analysis identified 5 type Ia patients with the missing long process of the incus and poor incudostapedial articulation. A literature search identified 113 type Ia patients (Table 3), which included fixation of the head of the malleus and the body of the incus, synostosis of the malleoincudal articulation, missing long Autogenous incus (30 cases): 1 case, 8 3 cases, 10 6 cases, 14 1 case, 15 19 cases 13 Autogenous (14 cases): 3 cases, 16 5 cases, 13 6 cases 12 Cartilage (5 cases): 5 cases 10 Teflon PORP (9 cases): 2 cases, 6 4 cases, 10 2 cases, 17 1 case 18 Others 9 Teflon TORP (5 cases) (silastic banding) 6 Teflon piston (1 case) 6 Modify cause prosthesis (2 cases) 19 ISJ prosthesis and hydroxyapatite bone cement (1 case) 20 Abbreviations: ISJ, incudostapedial joint; PORP, partial ossicular replacement prosthesis; TORP, total ossicular replacement prosthesis.…”

High‐resolution imaging of the human incudostapedial joint using synchrotron‐radiation phase‐contrast imaging

“…The incudostapedial joint (ISJ) connecting the incus and stapes in the middle ear significantly affects sound transmission to the cochlea (Funnell et al ., 2005; Zhang & Gan, 2011; Gan & Wang, 2015; Soleimani et al ., 2016; Soleimani et al ., 2017). Pathologies such as disarticulation and ankyloses of the joint are common and may cause hearing loss when vibrations can no longer be efficiently transmitted (Sim & Chang, 2008; Suzuki et al ., 2008). Recent experimental studies have shown that reduced stiffness of the ISJ, caused for example by a separation, could result in decreased stapes vibration at high frequencies (greater than 1 kHz) (Szymanski et al ., 2014).…”