Irreversible Hemichorea–Hemiballism in a Case of Nonketotic Hyperglycemia Presenting as the Initial Manifestation of Diabetes Mellitus

Roy, Ujjawal; Das, Shyamal Kumar; Mukherjee, Adreesh; Biswas, Debsadhan; Pan, Kaiwen; Biswas, Atanu; Panwar, Ajay

doi:10.7916/d8qz2b3f

Cited by 15 publications

(1 citation statement)

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“…Nonketotic hyperglycemic hemichorea (NH-HC) is a rare metabolic syndrome with a prevalence of less than one in 100,000 people [ 1 ]. NH-HC is characterized by a triad of nonketotic hyperglycemia, basal ganglia hyperintensity on MRI or high density on CT, and unilateral involuntary jerky (choreiform) movements affecting the upper and lower limbs contralateral to the side of the lesion [ 2 , 3 ]. NH-HC was first described by Bedwell in 1960 and presents typically in older diabetic patients [ 4 , 5 ].…”

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confidence: 99%

Atypical Imaging Findings of Nonketotic Hyperglycemic Hemichorea: A Case Report and Review of the Literature

Stevens¹,

Malone²,

Degueure³

et al. 2023

Cureus

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Nonketotic hyperglycemic hemichorea (NH-HC) is a rare condition presenting in the clinical setting. Brain imaging plays an important role in diagnosing NH-HC, which typically shows basal ganglia changes contralateral to the side of the hemiballismus/hemichorea. Only a few articles in the literature have reported normal pertinent magnetic resonance/CT findings in patients presenting with NH-HC. To the authors' knowledge, no cases in the literature have reported basal ganglia changes solely observed on CT but not on MRI in patients presenting with NH-HC. Herein, we describe a unique case in which a CT of a patient presenting with NH-HC demonstrated basal ganglia abnormalities with negative MRI findings.

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