Isolated Polycystic Liver Disease

Qian, Qi

doi:10.1053/j.ackd.2009.12.005

Cited by 59 publications

(57 citation statements)

References 76 publications

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“…Complications can also cause calcification of cyst walls. Associated dilatation of the intrahepatic and extrahepatic bile ducts may also be found in autosomal dominant polycystic liver disease [3,12].…”

Section: Santiago Et Almentioning

confidence: 99%

“…Most patients have no symptoms. Imaging studies usually show multiple liver cysts of various sizes, as large as 12 cm, in an enlarged liver [3,12]. Ultrasound images show cysts as anechoic lesions with well-defined thin walls.…”

Section: Santiago Et Almentioning

confidence: 99%

“…Liver cysts originate from biliary microhamartomas lined with functional biliary epithelium and do not communicate with the biliary tree. They usually become apparent after puberty and grow in size and number at variable rates with age [11,12]. Women are usually more severely affected [12,13].…”

Section: Santiago Et Almentioning

confidence: 99%

“…They usually become apparent after puberty and grow in size and number at variable rates with age [11,12]. Women are usually more severely affected [12,13]. The presence of more than 20 liver cysts (four, if there is a family history of cysts) is diagnostic [13] (Fig.…”

Section: Santiago Et Almentioning

confidence: 99%

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Congenital Cystic Lesions of the Biliary Tree

Santiago¹,

Loureiro²,

Curvo-Semedo³

et al. 2012

American Journal of Roentgenology

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Section: Santiago Et Almentioning

confidence: 99%

Section: Santiago Et Almentioning

confidence: 99%

Section: Santiago Et Almentioning

confidence: 99%

Section: Santiago Et Almentioning

confidence: 99%

See 2 more Smart Citations

Congenital Cystic Lesions of the Biliary Tree

Santiago¹,

Loureiro²,

Curvo-Semedo³

et al. 2012

American Journal of Roentgenology

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“…Qian (2010) [68] reported that isolated polycystic liver disease (PCLD) is an autosomal dominant disease with genetic and clinical heterogeneity. Rabbani et al (2010) [69] reported a case of a renal transplant recipient who suffered an isolated Mycobacterium tuberculosis infection of a native polycystic kidney.…”

Section: Diagnosis and Screeningmentioning

confidence: 99%

A Prospective Study on Clinical Profile of Autosomal Dominant Polycystic Kidney Disease (ADPKD) in Jammu for a Period of 1 Year

Kumar¹,

Kawoosa²,

Hamid³

et al. 2012

OJNeph

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The Present Study was conducted in department of Medicine, Govt. Medical College, jammu, Where a total of 41 patients-29 males and 12 females-fulfilled the inclusion criteria of ADPKD, were gathered during the period of 1 year starting from Nov. 2011 to Oct. 2012. All the patients were subjected to a detailed history, clinical examination and laboratory investigations. X-ray chest (PA view), ECG and ultrasound of abdomen for kidneys, liver and spleen were done. Intravenous pyelogram and CT scan of abdomen was done when a definitive diagnosis of (ADPKD) could not be made on abdominal ultrasound. Echocardiography was done to evaluate cardiac murmurs and associated mitral valve prolapse, based on standard criteria. Male to female patients with ADPKD was 2.42:1. Maximum 17 (41.5%) patients of both gender were seen in 30 -40 years age group, Family history of ADPKD was present in 18 (43.9%) patients; Hypertension, alone or in combination with renal failure, was present in 65.8% patients; Hypertension alone was present in 19 (46.3%) patients; 8 (19.5%) patients with hypertension had renal failure; Low back pain was present in 24 (58.5%) and abdominal pain in 22 (53.7%) patients; 15 (36.6%) patients presented with at least one episode of gross haematuria; Headache was experienced by 18 (43.9%) patients. On clinical examination, 24 (58.5%) were found to have palpable kidney and 10 (24.4%) had palpable liver. Spleen was palpable in 1 (2.4%) patient, Murmur of mitral valve prolapse was found in 2 (4.9%) Patients; 3 (7.3%) patients having left ventricular hypertrophy; mean Hb was 11.2 g/dL. The liver cysts were found in 24.4% of the patients; Out of 10 (24.4%) patients with hepatic cyst involvement, 1 patient each was found to have evidence of portal hypertension and evidence of hepatic cyst infection. In the present study, hypertension was most common presentation of this disease. So, control of hypertension is very important to prevent progression of this disease. Patients who are detected to have ADPKD should be regularly followed-up to prevent further progression by timely intervention. Also, family members of patients should be screened for disease and initiate treatment as early as possible.

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Benign Tumors, Nodules, and Cystic Diseases of the Liver

Bisceglie

Befeler

2011

Schiff's Diseases of the Liver

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Isolated Polycystic Liver Disease

Cited by 59 publications

References 76 publications

Congenital Cystic Lesions of the Biliary Tree

Congenital Cystic Lesions of the Biliary Tree

A Prospective Study on Clinical Profile of Autosomal Dominant Polycystic Kidney Disease (ADPKD) in Jammu for a Period of 1 Year

Benign Tumors, Nodules, and Cystic Diseases of the Liver

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