Jejunal obstruction as initial presentation of polyarteritis nodosa in a 13-month-old boy

Venuta, A; Ceccarelli, Pier Luca; Biondini, Diego; Montanari, Federica

doi:10.1016/j.jpedsurg.2011.03.084

Cited by 13 publications

(10 citation statements)

References 8 publications

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“…A case series reported by Venuta et al 10 reported eight patients with PAN and acute abdomen, and a mortality rate of 50%. A recent case report by Gomes et al 11 described the case of two boys with severe cramping abdominal pain, and findings of extensive intestinal necrosis as initial presentation of PAN.…”

Section: Discussionmentioning

confidence: 98%

Atypical Henoch-Schonlein purpura? Consider polyarteritis nodosa!

Braungart¹,

Campbell

Besarovic

2014

BMJ Case Reports

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We describe the case of a previously healthy 12-year-old boy admitted to a tertiary paediatric centre with the clinical diagnosis of Henoch-Schonlein purpura (HSP). Symptoms on admission included a generalised rash, colicky abdominal pain, hypertension, proteinuria and fresh rectal bleeding. Abdominal pain and distension worsened and serial ultrasounds suggested bowel ischaemia. He underwent repeat laparotomy and bowel resection, with slow improvement after the second laparotomy. The severity of systemic involvement (gastrointestinal, cardiac, renal and skin) made the initial diagnosis of HSP questionable. Immunohistochemistry of skin biopsies was negative for HSP. Histopathology of the bowel specimen revealed features of necrotising small and medium vessel vasculitis in keeping with polyarteritis nodosa.

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Section: Discussionmentioning

confidence: 98%

Atypical Henoch-Schonlein purpura? Consider polyarteritis nodosa!

Braungart¹,

Campbell

Besarovic

2014

BMJ Case Reports

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“…Acute intestinal obstruction due to AAB was reported in many cases [ 4 ] as a rare and severe abdominal manifestation of post-infectious, inflammatory, or collagen vascular diseases in the pediatric population and can be the only manifestation of disease activity.…”

Section: Discussionmentioning

confidence: 99%

Idiopathic congenital anomalous bands

Kerkeni

Aicha

Hamzaoui

2020

International Journal of Pediatrics and Adolescent Medicine

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Background and Objectives: Purpose There are various causes and associated conditions in anomalous bands. Idiopathic congenital anomalous bands are extremely rare. The use of the term “congenital bands” may, in reality, not describe the same situation. The study aims to report our series of idiopathic anomalous bands and proposes an accurate and consistent classification of anomalous bands in order to clarify the origin of each band. Methods This study, conducted from January 2005 to January 2018, included all patients admitted to the emergency departments with a clinical diagnosis of intestinal obstruction resulting from bands that have no identifiable embryological or acquired basis called “idiopathic”. Recorded operative findings included the site of obstruction and the operative procedure to relieve it. Results The sample consists of seven boys and three girls with age range from one day to 9 years with symptoms and signs indicative of intestinal obstruction. Surgical intervention was performed, and intraoperative findings revealed a thick and vascularized idiopathic band, in different locations, which was responsible for intestinal obstruction in all patients. Clinical courses were uneventful in eight cases. Conclusion Idiopathic anomalous congenital bands causing intestinal obstruction are not frequently encountered in surgical practice and these bands are often difficult to classify and define. We believe that our new classification is a practical communication tool for medical professionals to summarize and clarify the different types of anomalous bands.

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“…Venuta et al. [10] reported a pediatric PAN case and included a literature review. They described that four of seven reported cases died from gastrointestinal tract perforation or vascular occlusion.…”

Section: Discussionmentioning

confidence: 99%

A large superior mesenteric artery aneurysm and ileal obstruction: a rare presentation of polyarteritis nodosa in an infant

Shimizu

Tanaka

Takazawa

et al. 2019

Oxford Medical Case Reports

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Polyarteritis nodosa (PAN) is a rare form of vasculitis that occurs in childhood and affects small- and medium-sized arteries. Large aneurysms due to PAN can induce fatal complications like rupturing or occlusion of the affected arteries. Here, we report a case of a 4-month-old girl with PAN complicated by a large superior mesenteric artery aneurysm and ileal obstruction. We controlled her blood pressure to prevent the artery from rupturing. A combination of prednisolone, intravenous cyclophosphamide, and plasma exchange reduced the inflammation. She developed mechanical ileus due to ileum stricture and underwent bowel resection. Histopathological examinations revealed reparative arteritis around the healed ulcer. Her postoperative course was uneventful without further dilatation of the aneurysm. This case highlights the importance of intensive immunosuppressive therapy and appropriate blood pressure control in pediatric patients with PAN complicated by large aneurysms. Mechanical ileus can develop and may require surgical management even after remission of vasculitis.

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Jejunal obstruction as initial presentation of polyarteritis nodosa in a 13-month-old boy

Cited by 13 publications

References 8 publications

Atypical Henoch-Schonlein purpura? Consider polyarteritis nodosa!

Atypical Henoch-Schonlein purpura? Consider polyarteritis nodosa!

Idiopathic congenital anomalous bands

A large superior mesenteric artery aneurysm and ileal obstruction: a rare presentation of polyarteritis nodosa in an infant

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