Jugular Vein Phlebectasia (IJP): Surgically Manageable But Ignored Entity

Abstract

IJP is a rare, congenital, benign, isolated, sporadically occurring fusiform or saccular dilatation of Internal Jugular Vein (IJV) of unknown aetiology usually presenting as a unilateral neck mass. It is mostly seen in children and young adults. We report a 4 year old male presented to Expert ENT & Diagnostic Centre presenting with history of painless right neck swelling in the right carotid triangle first observed on crying with no history of trauma, facial congestion, chronic cough, difficulty in swallowing or breathing, non febrile, venous humps, heaviness or cessation of normal voice. Diagnosis of right IJP was made. Exploration and wrapping the dilated segment in polytetrafluoroethylene tube graft was done. Because of its rarity, this entity is frequently ignored or misdiagnosed. This case report intends to stress the importance of keeping IJP as differential diagnosis while dealing with such a swelling to avoid invasive investigations and inappropriate treatment.

Comprehensive review with pooled analysis on external and internal jugular vein aneurysm

“…Venorrhaphy was performed in six patients with an IJVA, and venorrhaphy with subsequent coating by a prosthesis was performed in three patients. [12][13][14][15][16] In 2012, Chua et al 17 described a hybrid approach to treat a patient with an IJVA. Two children, aged 6 and 8 years, respectively, were treated for a right-side IJVA with endoscopic transaxillary subfascial access with favorable cosmetic results.…”