Juvenile psammomatoid ossifying fibroma of the maxilla

Abstract

Ossifying fibroma (OF) is a benign fibro-osseous lesion. It is characterized by the presence of well-demarcated borders and cell-rich fibrosis and contains varying amounts of calcified tissues such as bone or cementum, or both. OF is classified into cemento-OF, juvenile trabecular OF and juvenile psammomatoid OF (JPOF) [1]. JPOF usually occurs before the age of 15 years, but it can also reportedly occur in adults [2-5]. It has a predilection for the paranasal sinuses and can occur in the maxilla, mandible, orbit, fronto-ethmoid complex, and frontal bone [2-8]. The diagnosis of JPOF is based on characteristic clinical manifestations, histological examination, and radiological characteristics. It is usually asymptomatic but short-term rapid growth of the mass can cause facial asymmetry, and when the maxilla, mandible, or both are affected it can also cause dental symptoms [2,7,8]. Histopathological JPOF exhibits dense cellularity with fibrous stroma and psammoma bodies. Radiological examinations have yielded a large spectrum of findings, including locularity, radiodensity, and cortical bone perforation [2,7]. Complete removal is the recommended treatment for JPOF because of its aggressive and locally invasive characteristics, but conservative local excision such as curettage, enucleation, or partial excision can be attempted depending on the patient's individual condition [2,3,9]. CASE REPORT A 20-year-old man was referred to our clinic by the department of otorhinolaryngology. Ten months prior he had noticed a mass on his right cheek, which was initially tender. Three months thereafter the mass had started increasing in size, and Archives of Craniofacial Surgery

Planificación digital en tratamiento de fibroma osificante juvenil psamomatoide maxilar. Presentación de un caso.

“…Cuando el maxilar, la mandíbula o ambos se ven afectados, también puede causar síntomas dentales. Entre los síntomas posteriores al rápido crecimiento dependiendo del compromiso del globo ocular o complejo nasal se puede generar exoftalmos, diplopía, alteración de la agudeza visual, obstrucción nasal uni o bilateral, anosmia, hiposmia, epistaxis o rinorrea 4,5 .…”

“…El fibroma osificante juvenil psamomatoide (FOJP) es una variante rara del fibroma osificante que puede ser localmente agresivo. Este presenta un rápido crecimiento a corto plazo y una alta tasa de recurrencia [2][3][4] . El FOJP generalmente se presenta en pacientes menores de 15 años, pero también puede ocurrir en adultos.…”

“…El FOJP generalmente se presenta en pacientes menores de 15 años, pero también puede ocurrir en adultos. Su ubicación prevalente son los senos paranasales, maxilar, mandíbula, órbitas, complejo frontoetmoidal y hueso frontal 4 .…”

“…Su histopatología muestra celularidad densa con estroma fibroso y cuerpos de psamoma. Se han descrito las siguientes características radiológicas del FOJP: locularidad, radiodensidad y perforación de hueso cortical 4,5 .…”

Giant fronto-spheno-orbitary juvenile psammomatoid ossifying fibroma: case report and literature review

“…JPOF is a highly vascular tumor which increases surgical risk due to signi cant bleeding [41]. Some authors found useful preoperative embolization, in those cases where the main blood supply came from the sphenopalatine artery or other less frequent extracranial arteries such as occipital [13].…”