Kayser-Fleischer Ring and Associated Cataract in Wilson's Disease

Tso, Mark O.M.; Fine, Ben S.; Thorpe, Harvey E.

doi:10.1016/0002-9394(75)90625-x

Cited by 48 publications

(15 citation statements)

References 6 publications

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“…The Kayser-Fleischer ring consists of orange to greenish pigments in Descemet's membrane in the peripheral 2 to 3 mm of the cornea (13) . Patients with Wilson's disease also demonstrate anterior lens capsular pigment, frequently in spokes along the Y-fissures, producing the "sunflower" cataract (14) .…”

Section: Discussionmentioning

confidence: 99%

Ocular copper deposition associated with monoclonal gammopathy of undetermined significance: case report

Tzelikis¹,

Laibson²,

Ribeiro³

et al. 2005

Arq. Bras. Oftalmol.

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Section: Discussionmentioning

confidence: 99%

Ocular copper deposition associated with monoclonal gammopathy of undetermined significance: case report

Tzelikis¹,

Laibson²,

Ribeiro³

et al. 2005

Arq. Bras. Oftalmol.

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“…São geralmente bilaterais e simétricos, mas existem relatos de anéis unilaterais (2)(3) . Estudos utilizando microscopia eletrônica e histoquímica (4) mostraram que os anéis de K-F são compostos por densas e não uniformes camadas contendo granulações de cobre com tamanhos variados, separadas por (5) . Estes depósitos, entretanto, não representam a maior parte do cobre presente na córnea em indivíduos com doença de Wilson.…”

Section: N T R O D U ç ã Ounclassified

“…A catarata consiste em um anel central na região pupilar do cristalino com cor e extensões em forma de pétalas que se assemelham ao girassol. O cristalino apresenta depósi-tos granulares semelhantes ao da córnea (5,17) . As manifestações neurológicas iniciais incluem tremores, disartria, sialorréia, incordenação e ataxia.…”

Section: Doença De Wilsonunclassified

Anéis de Kayser-Fleischer

Moreira¹,

Moreira²,

Fritscher³

et al. 2001

Arq. Bras. Oftalmol.

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“…12 Kayser-Fleischer rings disappear in the reverse order to their formation on treatment with Dpenicillamine'3 and after liver transplantation. '4 The direct source of copper for incorporation into Descemet's membrane is in dispute.…”

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confidence: 99%

Unilateral Kayser-Fleischer ring.

Innes¹,

Strachan²,

Triger³

1986

British Journal of Ophthalmology

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SUMMARY A patient is presented who had unrecognised Wilson's disease. He had developed a clinically obvious Kayser-Fleischer ring in only one eye. The eye without the corneal ring had been injured in childhood and had a low intraocular pressure. Possible mechanisms for formation of a Kayser-Fleischer ring are reviewed and the lack of Kayser-Fleischer ring in this case is discussed. Case historyThe patient first noticed a slight tremor of his hand and slight unsteadiness of gait at the age of 35. These symptoms progressed very slowly, and he was first seen by a neurologist at the age of 52. Signs present at that time were unsteadiness, cerebellar dysarthria, and ataxia of the hands, the right more than the left. The right eye was blind and divergent, the result of a penetrating injury by a dart at the age of 7.His past medical history revealed an episode of jaundice as a teenager and a urinary infection at the age of 40. Relevant family history was that his identical twin brother had died of hepatitis at the age of 47. He had also suffered from ataxia of a similar severity.Heredofamilial ataxia was diagnosed.

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Kayser-Fleischer Ring and Associated Cataract in Wilson's Disease

Cited by 48 publications

References 6 publications

Ocular copper deposition associated with monoclonal gammopathy of undetermined significance: case report

Ocular copper deposition associated with monoclonal gammopathy of undetermined significance: case report

Anéis de Kayser-Fleischer

Unilateral Kayser-Fleischer ring.

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