Keratosis Follicularis Spinulosa Decalvans Associated with Acne Keloidalis Nuchae and Tufted Hair Folliculitis

Janjua, Shahbaz A.; Iftikhar, Nadia; Paštar, Zrinjka; Hosler, Gregory A.

doi:10.2165/00128071-200809020-00009

Cited by 35 publications

(16 citation statements)

References 13 publications

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“…Furthermore, the thinning of the lateral eyebrows in their patient was also accompained by, diffuse follicular papules on the face and body. Other cases pointed to acne keloidalis as well as tufted folliculitis [17]. In our case, follicular tufting was also found in the areas where cicatricial alopecia had developed, and this type of tufting can occur as the result of diseases associated with superficial purulent inflammation that cause cicatricial alopecia of the scalp.…”

Section: Discussionsupporting

confidence: 65%

Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae

Topal¹,

Sahin²,

Berberoglu³

et al. 2014

Our Dermatol Online

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Keratosis follicularis spinulosa decalvans (KFSD) is a keratinization disorder characterized by diffuse follicular hyperkeratosis, progressive cicatricial alopecia, corneal dystrophy, and photophobia. Acne keloidalis nuchae (AKN) is a syndrome of chronic folliculitis that manifests as follicular-based pustules and papules on the occipital region of the scalp, which may eventually lead to cicatricial alopecia. Various diseases such as cutis laksa, deafness, aminoaciduria, mental retardation, and atopy have been reported to be associated with KFSD, but AKN is a rare cutaneous manifestation. Herein, we report the case of a patient with KFSD associated with AKN. He was presented to our clinic with follicular-based pustules and papules that had been progressively advancing for five years that were now manifesting as cicatricial alopecia.

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Section: Discussionsupporting

confidence: 65%

Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae

Topal¹,

Sahin²,

Berberoglu³

et al. 2014

Our Dermatol Online

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“…The lesions on the vertex tend to respond faster, and there is a decrease in pain and bleeding although the fibrotic lesions may still remain. Oral retinoids have been found useful in patients with associated folliculitis decalvans and low doses may be continued for up to a year 33,34…”

Section: Clinical Featuresmentioning

confidence: 99%

Acne keloidalis nuchae: prevalence, impact, and management challenges

Ogunbiyi¹

2016

CCID

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Acne keloidalis nuchae (AKN) also known as folliculitis keloidalis nuchae (FKN) is a chronic form of scarring folliculitis seen mostly in men of African descent. The term AKN is commonly used even though the condition is not a keloid, and the affected individuals do not have a tendency to develop keloids in other areas of the body. It is seen in post pubertal men and is rare after the age of 55 years. A few cases have been reported in females. which has been classified as a primary cicatricial alopecia since the exact cause of acne keloidalis (AK) remains unknown. However, a few inciting agents have been suggested which include androgens, inflammation, infection, trauma, genetics, and ingrowing hairs. AK shares some similar features with other forms of cicatricial alopecia and may occur together. Papules, pustules, and sometimes tumorous masses in the nuchal or occipital regions of the scalp hence the name “bumps” evolved in the environment. Despite its common occurrence, only a few seek help in hospital when lesions start to unsightly affect the individual’s quality of life. The presences of the keloidal lesions are more stressful compared to the resulting alopecia. Various attempts to reduce the bumps with corrosives, acids, and car engine oils lead to larger lesions or unsightly scars. Active lesions produce bleeding during haircuts. This is worrisome as a couple of individuals with active AK share shaving instruments at the barber shop and are at risk of acquiring or transmitting blood-borne infections. There is an urgent need to encourage safe shaving habits and treatment of lesions at onset so as to prevent unsightly lesions.

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“…[2] Less commonly reported features are atopy, deafness, mental retardation, acne keloidalis nuchae and tufted hair folliculitis , aminoaciduria and woolly hair. [8][9][10][11] KFSD simulates the ichthyosis follicularis alopecia photophobia (IFAP) syndrome. The latter is characterized by non-scarring alopecia, extensive KP, severe photophobia and corneal dystrophy.…”

Section: Discussionmentioning

confidence: 99%

Keratosis follicularis spinulosa decalvans in a female

Sequeira

Jayaseelan

2011

Indian J Dermatol Venereol Leprol

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Keratosis follicularis spinulosa decalvans (KFSD), is a rare follicular syndrome associated with widespread keratosis pilaris and progressive scarring alopecia. This genodermatoses often starts at infancy or early childhood with an X-linked mode of inheritance. Males are predominantly affected and females frequently show no disease or only a mild form. We describe this not so common entity of KFSD in a nine year old female child.

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Keratosis Follicularis Spinulosa Decalvans Associated with Acne Keloidalis Nuchae and Tufted Hair Folliculitis

Cited by 35 publications

References 13 publications

Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae

Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae

Acne keloidalis nuchae: prevalence, impact, and management challenges

Keratosis follicularis spinulosa decalvans in a female

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