Retrocaval ureter is a rare congenital anomaly, with the ureter passing posterior to the inferior vena cava. Its rarity and non-specific presentation poses a challenge to surgeons & radiologists in making the correct diagnosis. Though congenital,it commonly manifests in the third to fourth decade of life and very rarely in children. Symptomatic patients need surgical intervention. We present a child who presented with flank pain and diagnosed to have right hydronephroureterosis on radio imaging. During surgery, retrocaval anomaly was noticed. It was successfully treated by ureteral dissection, excision of the retrocaval segment and uretero-ureteral anastomosis.