Large intra-abdominal desmoid tumour posing diagnostic and therapeutic challenges, a case report

Burke, Eoghan; Saeed, Munir; Anant, Paul; Sami, Babur; Salama, Mohamed; Aliyu, Ibrahim

doi:10.1093/jscr/rjy304

Cited by 3 publications

(2 citation statements)

References 8 publications

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“…DT is benign, locally aggressive mesenchymal neoplasms derived from musculoaponeurotic stromal elements 1 . The peak incidence occurs between 25 and 35 years old.…”

Section: Figmentioning

confidence: 99%

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Life‐threatening presentation of complicated intra‐abdominal desmoid tumour in a young man without a family history of familial adenomatous polyposis

Vivekanandamoorthy

Choi

Toh

2022

ANZ Journal of Surgery

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Life-threatening presentation of complicated intra-abdominal desmoid tumour in a young man without a family history of familial adenomatous polyposis A 27-year-old Nepalese male presented to the emergency department with a 4-day history of worsening abdominal pain associated with vomiting, watery diarrhoea and fevers. He had no personal nor family history of note, particularly familial adenomatosis polyposis (FAP). He was tachycardic at 120 beats/min, and febrile to 38.4 C. He had a distended and tender abdomen with guarding and peritonism. His white cell count was 21.5 Â 10 9 /L and CRP was 161 mg/L. His abdominal computerised tomography (CT) demonstrated a large intra-abdominal mass with central necrosis

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“…DT is benign, locally aggressive mesenchymal neoplasms derived from musculoaponeurotic stromal elements 1 . The peak incidence occurs between 25 and 35 years old.…”

Section: Figmentioning

confidence: 99%

“…DT is benign, locally aggressive mesenchymal neoplasms derived from musculoaponeurotic stromal elements. 1 The peak incidence occurs between 25 and 35 years old. DT is reported to account for 0.03% of all neoplasms, and occur in 10-15% of patients with FAP.…”

mentioning

confidence: 99%

Life‐threatening presentation of complicated intra‐abdominal desmoid tumour in a young man without a family history of familial adenomatous polyposis

Vivekanandamoorthy

Choi

Toh

2022

ANZ Journal of Surgery

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Large desmoid tumour of the small bowel mesentery

et al. 2022

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A 74-year-old man was being investigated for a pancreatic insulinoma when an incidental mesenteric mass measuring 2.6 cm x 2.5 cm was noticed on CT imaging. A wait-and-see approach was decided on. Thirty-nine months later, the patient presented with symptoms of abdominal obstruction. CT images revealed the mesenteric mass filled majority of the abdominal cavity and measured 29 cm x 26 cm x 16 cm. The patient underwent an open bypass gastrojejunostomy which stopped working a few weeks later due to further compression by the tumour. A debulking surgery was performed: a right hemicolectomy and small bowel resection with excision of the desmoid tumour and bypass gastrojejunostomy. The tumour measured 12.6 kg and was macroscopically visualised to have a white cut surface with a focal translucent area. Microscopic analysis revealed bland spindle cells with pale eosinophilic cytoplasm showing no cytological atypia, in keeping with a mesenteric desmoid tumour. Currently, two and a half years from the debulking surgery, the patient remains well and in remission with planned surveillance.

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Desmoid tumor of Meckel's diverticulum presenting as intestinal obstruction

Mundada

Tote

Zade

2022

Journal of Cancer Research and Therapeutics

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Meckel's diverticulum (MD) is among the many known congenital malformations of intestine. It is seen in approximately 2% of the population. Desmoid tumors are unusual. They are unique, well-differentiated, and fast-growing musculoaponeurotic fibromatosis tumors, contemplated as Grade 1 fibro sarcoma. They offer exclusive management challenges to surgeons. The most common presentation of desmoid tumors is of painless masses with sluggish growth. Rarely, they may present as intestinal obstruction leading to surgical emergency. We present the only case in history till date along with review of the relevant literature of a 65-year-old gentleman who presented to us with features of intestinal obstruction who successfully underwent elective segmental resection of ileum containing MD with its desmoid tumor. A multimodality approach is needed to tackle such kind of diseases with a team comprising oncosurgeons, oncophysicians, and radiation oncologist to design a standard treatment protocol.

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Large intra-abdominal desmoid tumour posing diagnostic and therapeutic challenges, a case report

Cited by 3 publications

References 8 publications

Life‐threatening presentation of complicated intra‐abdominal desmoid tumour in a young man without a family history of familial adenomatous polyposis

Life‐threatening presentation of complicated intra‐abdominal desmoid tumour in a young man without a family history of familial adenomatous polyposis

Large desmoid tumour of the small bowel mesentery

Desmoid tumor of Meckel's diverticulum presenting as intestinal obstruction

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