Large vestibular aqueduct syndrome treated by hyperbaric oxygen

Sudden Sensorineural Hearing Loss in the Only Hearing Ear: Large Vestibular Aqueduct Syndrome

“…The hearing loss is mild at the few years of life, but it worsens with an average of 4 dB/year causing a profound hearing loss in the adulthood [9]. The characteristic hearing loss is a progressive or fluctuating type sensorineural hearing loss; acute deteriorations can be seen especially with mild head trauma [6, 9]. The higher pressure of cerebrospinal fluid transmission to the inner ear by enlarged VA may be the main reason of the sensorineural hearing loss [6].…”

“…SHL occurring in the only hearing ear is a more serious problem, since it increases patient's morbidity and the sequel in the only hearing ear can affect the patient's social life dramatically with interrupting the verbal communication. SSHL in the only hearing ear cases are rarely published in the English literature [2–6] and most of these cases are idiopathic. In this case report we presented a large vestibular aqueduct syndrome (LVAS) patient admitting with a sudden hearing loss in the only hearing ear.…”

Hyperbaric oxygen therapy for sudden sensorineural hearing loss in large vestibular aqueduct syndrome

“…The original case report involved a 14-year-old girl with acute, right-sided hearing loss. 1 She was administered intravenous steroids for 7 days, followed by 7 days of alprostadil. She had no hearing improvement, and an auditory brainstem response could not be recognised.…”

The large vestibular aqueduct – case report and review of the literature

“…However, these are isolated cases and the history of hearing losses in LVA patients must be taken into consideration. Nakashima et al [34] reported on treatment with hyperbaric oxygen therapy in a teenager with bilateral LVA and a sudden hearing loss. After 22 sessions, the patient's sudden hearing loss exhibited thresholds comparable to those prior to the hearing loss, and the hearing remained stable during an 8-month follow-up period.…”