Late Results after Repair of Complete Atrioventricular Canal.

Left bundle pacing in a patient with atrioventricular canal defect presenting with atrial standstill and junctional bradycardia

“… 4 , 13 Clinically, atrial standstill manifests as symptomatic bradycardia with dizziness, syncope, dyspnea, heart failure, and stroke or systemic embolism. 4 , 8 , 9 In the case that we present here, atrial standstill was likely caused by her extensive prior cardiac surgery and biatrial maze procedure and likely contributed to recurrent admissions for acute decompensated heart failure.…”

“…Atrial standstill is a rare condition defined by the lack of atrial electrical activity and mechanical function, and it may be intermittent or permanent, partial or total, and congenital or acquired (myocardial disease or metabolic/toxic). 1 , 4 , 8 , 9 Myocardial causes of acquired atrial standstill include surgical myocardial injury, 10 , 11 acute myocarditis, myocardial infarction, 12 cardiac sarcoidosis, mitral valve stenosis, rheumatic heart disease, and muscular dystrophy. Histologically, atrial standstill is characterized by fibroelastosis and fatty infiltration in the atrium.…”

Left Bundle Pacing in a Patient with Atrio-Ventricular Canal Defect Presenting with Atrial Standstill and Junctional Bradycardia

“…Atrial standstill is a rare condition defined by the lack of atrial electrical and mechanical function, and it may be intermittent or permanent, partial or total, and congenital or acquired (myocardial disease or metabolic/toxic). [1][2][3]6 Myocardial causes of acquired atrial standstill include surgical myocardial injury, 7,8 acute myocarditis, 9,10 myocardial infarction, 11 cardiac sarcoidosis, 12 mitral valve stenosis, 13 rheumatic heart disease, 14 and muscular dystrophy. 15 Histologically, atrial standstill is characterized by fibroelastosis and fatty infiltration in the atrium.…”

“…4,6,16 Clinically, atrial standstill manifests as symptomatic bradycardia with dizziness, syncope, dyspnea, heart failure, and stroke or systemic embolism. [1][2][3]6 In the case that we present here, atrial standstill was likely caused by her extensive prior cardiac surgery and biatrial maze procedure and likely contributed to recurrent admissions for acute decompensated heart failure.…”

“…Patients with atrioventricular canal defects that undergo corrective surgery can experience disturbance of sinus node and atrioventricular node function with rates up to 19 and 25%, respectively. 1,2 Atrial standstill was first documented in a case report by Chavez et al in 1946, and constitutes a rare clinical condition defined by the absence of atrial electrical and mechanical activity. 3 Atrial standstill is characterized by fibroelastosis and fatty infiltration in the atrium, 4 and is a barrier in successful implantation of atrial leads.…”