Left atrial approach to close the atrial septal defect type II in case of right lung agenesis with extreme dextroversion

Abstract

This paper presents a case of a rare combination of right lung agenesis and atrial septal defect type II (ASD II). Successful surgical repair of ASD II was performed at the age of six years with total circulatory arrest (TCA) and deep hypothermia, because of difficult approach. Computed tomography and intraoperative findings are described. From patho-embryological consideration, defects in the primitive respiratory apparatus in embryo stages were presumably responsible for agenesis of the lung. The patient was found to have a very short stump of the right pulmonary artery, but this malformation seems to be secondary.

Neonatal repair of total anomalous pulmonary venous connection accompanied by unilateral lung agenesis and Goldenhar syndrome: a case report

“…Pietrzykowski et al [ 5 ] observed that venous cannulation was challenging via a median sternotomy to gain access to structures that were more posteriorly positioned than usual. In our view, a median sternotomy scored over posterolateral thoracotomy to anastomose the pulmonary venous chamber and the left atrium in our patient.…”

Pulmonary Agenesis and Associated Pulmonary Hypertension: A Case Report and Review on Variability, Therapy, and Outcome

“…Surgical therapy includes correction of the associated cardiac defects, particularly if these are severe or cause significant morbidity. 20 21 22 Tracheobronchial compression has been addressed by aortopexy, 23 and tracheoplasty on and off ECMO. 5 24 25 Implantation of a tissue expander for pulmonary agenesis was first described in 1995 in a report from Berlin, Germany.…”