Life Threatening Gastrointestinal Bleeding in Klippel Trenaunay Syndrome

Thosani, Nirav; Reddy, Sheila; Scott, Larry D.

doi:10.14309/00000434-201110002-00897

Cited by 2 publications

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“…KTS diagnosis depends on physical and imaging examinations. Other site involvement causing compression and bleeding has also been reported, and include; the central nervous system [5], the gastrointestinal tract [6], the uterus [7] and the urinary bladder [8].…”

Section: Discussionmentioning

confidence: 99%

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Gastrointestinal bleeding with Klippel–Trenaunay syndrome: a case report

2021

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Background Gastrointestinal bleeding caused by gastrointestinal tract involvement in patients with Klippel–Trenaunay syndrome (KTS) is extremely rare and often overlooked. Case presentation A 9-year-old girl who presented with chronic gastrointestinal bleeding was admitted to our hospital. Laboratory examinations revealed microcytic hypochromic anemia and a positive fecal occult blood test. Computed tomography (CT) of the lower limbs combined with physical examination confirmed KTS. The pelvic CT showed concentric thickening of the sigmoid colon and rectum, with progressive enhancement after the administration of a contrast agent. Colonoscopy demonstrated vascular malformations of the sigmoid colon and rectum. The patient was finally diagnosed with KTS with gastrointestinal tract involvement. The patient improved after receiving conservative treatment. Conclusions A suspicion of gastrointestinal tract involvement as an etiology for gastrointestinal bleeding should not be overlooked in patients with KTS. Endoscopy and imaging modalities can synergistically help diagnose this condition.

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Section: Discussionmentioning

confidence: 99%

“…The sigmoid colon and rectum are the most commonly affected areas. Clinical manifestations range from symptom-free to life-threatening gastrointestinal bleeding [6,10]. Thus, condition awareness is paramount for appropriate clinical management.…”

Section: Discussionmentioning

confidence: 99%

Gastrointestinal bleeding with Klippel–Trenaunay syndrome: a case report

2021

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“…Venous thromboembolism is the most common complication due to low-flow vascular malformation of KTS ( 5 ). Although, there were case reports on hemorrhagic complications of KTS, this bleeding often occurred to the visceral organs affected by venous malformations, such as skin lesions ( 6 ), gastrointestinal tract ( 7 ), and genitourinary system ( 8 ). Although, a nationwide cross-sectional study demonstrated that women with KTS also suffered from hemorrhage complications, the hemorrhagic complication was mainly postpartum bleeding at special periods, such as in pregnancy and in early postpartum ( 9 ).…”

Section: Introductionmentioning

confidence: 99%

Case Report: Life-Threatening Post-operative Hemorrhage in Klippel–Trenaunay Syndrome Associated With Hypofibrinogenemia

Yang

Liu

et al. 2021

Front. Med.

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Klippel–Trenaunay Syndrome (KTS) is a rare congenital disorder, characterized by venous and lymphatic malformations of the skin, soft tissue, and bone, causing limb hypertrophy. Although, a ruptured hemorrhagic corpus luteum is a rare condition in women of reproductive age, it can result in lethal outcomes. Here, we have described a patient with KTS and hypofibrinogenemia who went through recurrent lethal postoperative bleeding due to a ruptured hemorrhagic corpus luteum. This case suggested that conservative therapy might be the first choice and effective therapy for the patients with KTS, who suffered from bleeding complications of surgical therapy.

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Life Threatening Gastrointestinal Bleeding in Klippel Trenaunay Syndrome

Cited by 2 publications

References 0 publications

Gastrointestinal bleeding with Klippel–Trenaunay syndrome: a case report

Gastrointestinal bleeding with Klippel–Trenaunay syndrome: a case report

Case Report: Life-Threatening Post-operative Hemorrhage in Klippel–Trenaunay Syndrome Associated With Hypofibrinogenemia

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