Light-guided surgery to repair coronary sinus orifice atresia with left superior vena cava

Abstract

An 8-month-old male with coronary sinus orifice atresia, left superior vena cava, and single ventricle underwent light-guided coronary sinus unroofing concomitant with bidirectional cavopulmonary anastomosis to circumvent coronary sinus hypertension. During surgery, a 2.25 Fr angioscopic catheter was inserted into the coronary sinus via the left superior vena cava. The coronary sinus, lit by the illumination obtained from the catheter, was readily located from the left atrial interior, and unroofed. Light-guided coronary sinus unroofing is an easy, safe, and quick technique for the creation of unobstructed coronary sinus drainage in patients with coronary sinus orifice atresia and left superior vena cava.

Bidirectional coronary venous return in the partial unroofed coronary sinus syndrome complicated by coronary sinus orifice atresia

“…2 Furthermore, coronary venous flow returned to the left atrium through the unroofed coronary sinus during balloon occlusion, which is like a single ventricle physiology. 7 This circulation has the risk of cyanosis and paradoxical embolism. Although ischaemic change or cyanosis did not occur during test occlusion in our patient, we decided not to perform the persistent left superior caval vein ligation.…”

Single-Stage Fontan Operation in a Patient With Coronary Sinus Ostium Atresia

“…In single ventricle cases, the clinical picture may be complicated. [1][2][3] In this report, we present a case of CSOA that was surgically repaired during the Fontan operation.…”