Limited Dorsal Myeloschisis Associated with Multiple Vertebral Segmentation Disorder

Abstract

A 3-year-old girl was admitted to our department with spina bifida occulta. At birth, thoracic dysplasia with severe respiratory dysfunction and a soft pedunculated mass connecting with an intradural mass were noted. The patient did not start to walk and partial removal of the intradural mass was performed via a laminectomy of the fused vertebrae. There was no boundary between the spinal cord and the mass and the histological diagnosis of this mass was connective tissue. The anomalies in this case were considered to be multiple vertebral segmentation disorder (MVSD) and limited dorsal myeloschisis. The coincidence of these anomalies might suggest the causal genesis of MVSD.

Missed limited dorsal myeloschisis: an unfortunate cause for recurrent tethered cord syndrome

“…Pang et al [14] further described the association of LDMs with lipomas, dermal sinus tracts and split cord malformations. LDMs are now known to be associated with multiple vertebral segmentation defects (MVSDs) too [15]. The association of non-terminal myelocystoceles with multiple other defects have been known even before the entity was described [16].…”

The Role of Intraoperative Electromyographic Monitoring in Lumbosacral Lipomas

“…However, this varies greatly from person to person and there is a high percentage of multiple subtypes that coexist within the same subject (17,26,27,36). The time and manner in which this spontaneous deterioration manifests (a slow progression or an acute onset) is unknown for each individual case, and there is much controversy regarding whether to perform surgery before or after the onset of such possible deterioration (4,9,38,39,42,56).…”