Localized retroperitoneal Rosai-Dorfman-Destombes disease as a cause of fever of unknown origin in adults. Case report and review of the literature

Popivanov, Georgi; Baymakova, Magdalena; Bochev, Pavel B.; Penchev, D.; Konaktchieva, Marina; Mutafchiyski, Ventsislav

doi:10.1016/j.ijscr.2022.107414

Cited by 2 publications

(2 citation statements)

References 15 publications

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“…Extranodal lesions accompany the presentation in 43% of patients with RDD. 4 , 5 In addition, 10% of cases of extranodal RDD occur concurrently with autoimmune diseases, warranting closer attention. 6 In particular, RDD has been documented to co-occur with systemic lupus erythematosus, idiopathic juvenile arthritis, autoimmune hemolytic anemia, rheumatoid arthritis, and autoimmune leukoproliferative disease.…”

Section: Discussionmentioning

confidence: 99%

Extranodal Rosai–Dorfman disease manifesting as Sjögren’s syndrome combined with panuveitis and hypertrophic pachymeningitis: a case report and review of literature

Xu,

Huang,

Dong

et al. 2024

J Int Med Res

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Rosai–Dorfman disease (RDD) is a rare non-Langerhans cell histiocytosis characterized by massive lymphadenopathy and systemic extranodal lesions. We present the case of a 28-year-old woman who presented with recurrent blurred vision in her right eye for 3 months. She developed blindness and atrophy in her left eye a decade prior to presentation. She subsequently developed headache, fever, and impaired mental status. Cranial magnetic resonance imaging indicated hypertrophic pachymeningitis (HP), and 18F-fluoro-2-deoxy-2-d-glucose (FDG) positron emission tomography/computed tomography revealed significant FDG uptake in the left dura mater. Autoimmune testing revealed elevated anti-nuclear, anti-SS-A, and anti-SS-B antibody levels. Incisional biopsy of the atrophic eyeball revealed RDD with marked polyclonal plasmacytosis. The patient was diagnosed with RDD accompanied by multisystem involvement, including Sjögren’s syndrome (SS), panuveitis, and HP. Treatment with methylprednisolone for several weeks resulted in significant improvement. This is the first reported case of RDD presenting with SS in combination with panuveitis and HP. Although RDD is rarely diagnosed in young patients, interdisciplinary collaboration is essential to prevent a delayed diagnosis.

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Section: Discussionmentioning

confidence: 99%

Extranodal Rosai–Dorfman disease manifesting as Sjögren’s syndrome combined with panuveitis and hypertrophic pachymeningitis: a case report and review of literature

Xu,

Huang,

Dong

et al. 2024

J Int Med Res

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“…Rosai–Dorfman disease (RDD) is a rare, benign, non-Langerhans cell histiocytosis with massive lymphadenopathy of uncertain etiology and a prevalence of 1:200,000. 1 RDD is commonly characterized by massive, painless, non-tender, bilateral cervical lymphadenopathy, and can be associated with systemic symptoms such as fever, weight loss, malaise, leukocytosis, and anemia. 2 RDD predominantly affects children and young adults with an average age of onset of 20.6 years.…”

Section: Introductionmentioning

confidence: 99%

Successful anesthesia management with inhalation anesthesia in Rosai–Dorfman disease: a case report

Zhang,

Zhou,

Liu

et al. 2023

J Int Med Res

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Rosai–Dorfman disease (RDD) is a rare, benign, non-Langerhans cell histiocytic proliferative disease. RDD with central nervous system involvement is extremely rare. Surgical excision is generally regarded as the appropriate treatment of choice for this disease, especially when the lesion causes neurological compression. RDD can be accompanied by systemic symptoms, such as malaise, fever, weight change, leukocytosis, anemia, and hormonal disturbance, which may be challenging during general management. Little is known regarding peri-anesthesia management of this rare disease. We report a case of a patient in his 20s who had recurrent RDD and had general anesthesia with perioperative management. He was obese and hepatic insufficiency. This case report adds to the literature regarding the perioperative anesthetic management of RDD with central nervous system involvement.

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Localized retroperitoneal Rosai-Dorfman-Destombes disease as a cause of fever of unknown origin in adults. Case report and review of the literature

Cited by 2 publications

References 15 publications

Extranodal Rosai–Dorfman disease manifesting as Sjögren’s syndrome combined with panuveitis and hypertrophic pachymeningitis: a case report and review of literature

Extranodal Rosai–Dorfman disease manifesting as Sjögren’s syndrome combined with panuveitis and hypertrophic pachymeningitis: a case report and review of literature

Successful anesthesia management with inhalation anesthesia in Rosai–Dorfman disease: a case report

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