Long-term follow-up study of West syndrome: differences of outcome among symptomatic etiologies

Hamano, Shin‐ichiro; Tanaka, Manabu; Mochizuki, Mika; Sugiyama, Nobuyoshi; Eto, Yoshikatsu

doi:10.1067/s0022-3476(03)00323-8

Cited by 32 publications

(27 citation statements)

References 21 publications

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“…The different outcome of West syndrome depends on the etiology [89]. A short treatment interval from the beginning of the symptoms seem to be associated with a favourable outcome.…”

Section: Prognosismentioning

confidence: 99%

Infantile spasms: review of the literature and personal experience

Fois

2010

Ital J Pediatr

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This epileptic disorder has become a classic topic for neuropediatricians and the interest is documented by the large number of publications on this subject.The relative frequency among the epileptic syndromes is an another reason why not only neuropediatricians but also general pediatricians must be fully informed about diagnostic, clinical, imaging and genetic aspects.Early diagnosis is of paramount importance in order to obtain even complete results in patients with so called idiopathic situations. A number of problems are still to be solved. There is no agreement on the type and the schedule of treatment. A common denominator about this problem is not jet available even if some advances in this regard have been accomplished. Of paramount importance is an accurate clinical and laboratory examination as a prerequisite regarding prognosis and results of therapy in every single case.However, even if more than 170 years have elapsed since the first communication of dr. West on the peculiar syndrome that his child was suffering of, the interest of scientists on this subject has now been enriched and rewarded.

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“…The different outcome of West syndrome depends on the etiology [89]. A short treatment interval from the beginning of the symptoms seem to be associated with a favourable outcome.…”

Section: Prognosismentioning

confidence: 99%

Infantile spasms: review of the literature and personal experience

Fois

2010

Ital J Pediatr

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“…There have been relatively few reports regarding the long-term prognosis of epilepsy and its impact on the daily life of patients with WS [4,5]. Both the prognosis of epilepsy and cognitive outcomes of WS are related to the etiological characteristics of the syndrome, as cryptogenic WS (cWS) has a more favorable outcome than symptomatic WS (sWS) [6][7][8][9]. Normal or subnormal cognitive development has been reported in approximately 25% of adult patients with previous WS [5].…”

Section: Introductionmentioning

confidence: 99%

Long-term outcomes in patients with West syndrome: An outpatient clinical study

Güveli

Çokar

Dörtcan

et al. 2015

Seizure

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“…7,8 Although the outcome of patients with normal MRI is better than the outcome of those with abnormal MRI, the outcome can vary even among patients with normal MRI. Developmental and seizure outcomes are largely dependent on the etiology.…”

Section: Discussionmentioning

confidence: 99%

Popliteal Angle in Infants With West Syndrome

et al. 2006

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The aim of this study was to clarify the relationship between neurologic findings and outcome of patients with West syndrome, focusing on the popliteal angle. The complete neurologic examination, including an assessment of the popliteal angle and muscle tone, was performed on 45 patients with West syndrome. A tight popliteal angle was determined when it was 120 degrees or less. In all 45 patients, abnormal muscle tone was not correlated with any variables. A tight popliteal angle was correlated with seizure persistence, cerebral palsy, and abnormality on magnetic resonance imaging (MRI), as well as severe developmental delay. When limited to the patients with developmental delay, a tight popliteal angle was correlated with severe developmental delay, cerebral palsy, and MRI abnormality, although abnormal muscle tone was not correlated with any items. In the delay group, eight patients had a tight popliteal angle with normal muscle tone. Among them, severe developmental delay was seen in seven (88%), seizure persistence in five (63%), and MRI abnormality in five (63%). These results suggest that a tight popliteal angle might be an indicator of poor neurologic outcome in patients with West syndrome.

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Long-term follow-up study of West syndrome: differences of outcome among symptomatic etiologies

Cited by 32 publications

References 21 publications

Infantile spasms: review of the literature and personal experience

Infantile spasms: review of the literature and personal experience

Long-term outcomes in patients with West syndrome: An outpatient clinical study

Popliteal Angle in Infants With West Syndrome

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