Maladie de Darier linéaire dans une fratrie

Linear Darier's disease: A case with bilateral presentation

“…Type 1 form retains the heterozygosity of mutation and the skin outside the segmental lesion is normal, whereas Type 2 is rarer, more severe, and is characterized by linear streaks over a background of generalized Darier's disease. [ 6 7 8 ] Our case probably belonged to the Type 1 form because it was localized and the surrounding skin was also normal.…”

A case of zosteriform Darier′s disease with seasonal recurrence

“…[5] Since then, various localized variants like unilateral, linear, segmental or zosteriform have been described. [456789] The skin lesions in the localized variants are usually confined to a limited area and other features that are associated with classical DD are usually absent. The lack of family history, absence of other signs of DD and the limited distribution of the lesions favor a nevoid origin.…”

“…If there is associated gonadal mosacism, a patient with segmental manifestation may have an offspring with generalized DD. [9]…”

“…[4] Localized pattern of DD was first reported in 1906. [5] Since then, many localized variants like localized, unilateral, linear,segmental or zosteriform DD[456789] have been described. We present a case of zosteriform DD confined to the right infra-mammary region in an adult female.…”