Maladie de Hirschsprung : attitude pratique

Boman, Françoise; Corsois, L.; Paraf, F

doi:10.1016/s0242-6498(04)94013-8

Cited by 3 publications

(2 citation statements)

References 84 publications

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“…In our country, physicians seek non-invasive techniques, such as CE screening which is less invasive, readily available, and provides a prompt diagnosis. CE provides a road map to surgeons by ascertaining the transition zone (TZ) and helps in pre-surgical planning [3][4]. Anorectal manometry is unavailable in most centers in Pakistan.…”

Section: Introductionmentioning

confidence: 99%

Usefulness of Delayed Films of Contrast Enema for Detecting Hirschsprung’s Disease

Sajjad¹,

Hilal²,

Khandwala³

et al. 2019

Cureus

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Background Contrast enema (CE) in Hirschsprung's disease (HD) provides a road map to surgeons by ascertaining the transition zone (TZ) and helps in pre-surgical planning. In our institute, we use CE as the initial investigation for HD and carry on till the whole colon is fully distended, followed by a 24-hour abdominal film which is also a part of the international protocol. The main aim of this study was to evaluate the usefulness of this 24-hour delayed film in detecting HD, compare it with gold-standard biopsy results, and to evaluate other imaging features of contrast enema for diagnosis of HD in our tertiary-care hospital in Pakistan.

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Section: Introductionmentioning

confidence: 99%

Usefulness of Delayed Films of Contrast Enema for Detecting Hirschsprung’s Disease

Sajjad¹,

Hilal²,

Khandwala³

et al. 2019

Cureus

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“…Although the initial diagnosis is mainly based on clinical history and examination, followed only afterwards by pathological assessment ( 4 ), radiographic contrast assessment may be useful in diagnosis ( 5 , 6 ). The risks associated with rectal biopsy, such as perforation, scar, stricture, bleeding and also anesthesia-related adverse effects, results in seeking several non-invasive techniques, such as imaging methods ( 7 , 8 ). A plain radiography may demonstrate a transition zone between a gas-filled colon and a non-dilated proximal colon, as a funnel-shaped region.…”

Section: Introductionmentioning

confidence: 99%

Diagnostic Accuracy of Radiologic Scoring System for Evaluation of Suspicious Hirschsprung Disease in Children

et al. 2015

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Background:In 1996, Donovan and colleagues represented a scoring system for better prediction of Hirschsprung disease (HD).Objectives:Our objective was to devise another scoring system that uses a checklist of radiologic and clinical signs to determine the probability of HD in suspicious patients.Patients and Methods:In a diagnostic accuracy study, 55 children with clinical manifestations of HD that referred to a training hospital from 1998 to 2011 were assessed. A checklist was used to evaluate the items proposed by contrast enema (CE), based on six subscales, including transitional zone, rectosigmoid index (RSI), irregular contractions in aganglionic region, cobblestone appearance, filling defect due to fecaloid materials and lack of meconium defecation during the first 48 hours after birth. The patients were classified as high score and low score. Sensitivity, specificity, positive predictive value and negative predictive value of our scoring system were calculated for identifying HD, in comparison with pathologically proved or ruled out HD.Results:Of the 55 patients, 36 (65.4%) cases had HD and 19 (34.6%) cases were without HD. In the HD group, 32 patients showed high scores and four patients had low scores. The sensitivity and specificity of our diagnostic scoring system were 88.9% (95% CI: 78.6% - 99.1%) and 84.2% (95% CI: 68.7% - 100%), respectively. Moreover, positive predictive value (PPV) and negative predictive value (NPV) were 91.4% (95% CI: 82.1% - 100%) and 80% (95% CI: 62.5% - 97.5%), respectively.Conclusions:Our new scoring system of CE is a useful diagnostic method in HD. If a patient’s score is high, that patient is highly suspicious to HD and reversely, when one’s score is low, the patient presents a reduced probability to be diagnosed with HD.

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Üst gastrointestinal sistem kanaması ile gelen Hirschprung hastası: Olgu Sunumu

Nar¹,

Uyanıkoğlu²,

Aydoğan³

et al. 2015

Endoskopi Gastrointestinal

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A Hirschsprung patient admitted with upper gastrointestinal bleeding: case reportÜst gastrointestinal kanama gastrointestinal sistemin en sık görülen acillerindendir. Peptik ülser en sık sebeptir. Hirschsprung hastalığı sindirim sisteminin distal kısımlarında sinir pleksuslarında nöronal hücre yokluğuyla tanımlanan konjenital bir hastalıktır. Hastaların %80'inde rektum ve sigmoid kolon, bazı olgularda daha yaygın tutulum vardır. Neonatal dönemde meydana gelen alt gastrointestinal sistem obstrüksiyonlarında ya da bazı olgularda erken çocukluk çağında uzamış ağır kabızlık durumlarında Hirschprung hastalığından şüphelenilir. Burada hematemez şikayeti ile gelen, duodenal ülsere bağlı üst gastrointestinal kanama tespit edilen 52 yaşında, erkek Hirschprung hastası sunulmuştur. Anahtar kelimeler: Üst gastrointestinal kanama, HirschprungUpper gastrointestinal bleeding is the most common gastrointestinal emergency. Peptic ulcer is the most common cause. Hirschsprung disease is defined by the congenital absence of neuronal cells in the nerve plexuses in the distal part of the digestive tract. The disease affects the rectum and sigmoid colon in 80% of cases, or is more extensive. Hirschsprung disease is suspected in cases of low gastrointestinal obstruction in the neonatal period, or in cases of chronic severe constipation in childhood. We report a 52-year-old male Hirschsprung patient who admitted with hematemesis due to duodenal ulcer in upper gastrointestinal bleeding. Keywords: Upper gastrointestinal bleeding, Hirschsprung GİRİŞÜst gastrointestinal kanama (ÜGK), Treitz ligamentine kadar olan proksimal duodenum ile üst özofagus sfinkteri arasında lümen içine olan kanamayı ifade eder. Şiddeti; subklinik gizli bir kanamadan abondan kanamaya, kronik anemiden akut hipovolemik şoka kadar değişebilen geniş bir spektrumu kapsar (1). Akut ÜGK, sık karşılaşılan önemli mortalite ve morbidite nedenlerindendir. İnsidansı yıllık hastane başvu-rularının 100000'de 50-150'si arasında değişmektedir (2,3). Farmakolojik ve girişimsel tedavi yöntemlerindeki tüm gelişmelere rağmen mortalite %2-10 arasındadır (4,5). ÜGK'ların yaklaşık %50'sinin nedeni peptik ülserdir. Hastaların %30-50'sinde nonsteroid antiinflamatuvar ilaç (NSAİİ) kullanımı mevcuttur. Özellikle yaşlı hastalarda NSAİİ'lara bağlı ÜGK riski yüksektir (6,7).Hirschsprung hastalığı sindirim sisteminin distal kısımların-da sinir pleksuslarında nöronal hücre yokluğuyla tanımlanan konjenital bir hastalıktır. Hastalık %80 rektum ve sigmoid kolonu, bazı olgularda daha yaygın kısmı etkiler. Neonatal dönemde meydana gelen alt gastrointestinal sistem obstrük-siyonlarında ya da bazı olgularda erken çocukluk çağında uzamış kabızlık durumlarında Hirschprung hastalığından şüphelenilir. Tanısı submukozayı da içeren rektal biyopsi ile konur. Tedavisi genellikle normal olarak inerve edilen barsak segmentinin anal kanala anastomozudur (8). Hastalığın genel popülasyondaki insidansı 1/5000 olup, erkeklerde 4 kat daha sık görülür. Genellikle infant döneminde veya çocukluk çağında tanınan bu hastal...

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Maladie de Hirschsprung : attitude pratique

Cited by 3 publications

References 84 publications

Usefulness of Delayed Films of Contrast Enema for Detecting Hirschsprung’s Disease

Usefulness of Delayed Films of Contrast Enema for Detecting Hirschsprung’s Disease

Diagnostic Accuracy of Radiologic Scoring System for Evaluation of Suspicious Hirschsprung Disease in Children

Üst gastrointestinal sistem kanaması ile gelen Hirschprung hastası: Olgu Sunumu

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