Malformations pulmonaires congénitales, le point de vue du radiologue

Bobbio, Antonio; Millischer-Bellaïche, A.-E.; Lambot, Karen; Breton, Sylvain; Brunelle, Françis

doi:10.1016/j.rmr.2011.10.976

Cited by 9 publications

(5 citation statements)

References 51 publications

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“…Te diagnosis of pulmonary agenesis can be made before or after birth. In children or adults, the standard radiograph usually shows an opaque hemithorax, distension of the contralateral lung, part of which is often herniated on the other side of the midline with more or less severe pinching of the homolateral intercostal spaces [1]. However, thoracic computed tomography with an injection of contrast medium remains the reference examination to make the diagnosis, allowing visualization of the agenesis of the pulmonary artery [1,5].…”

Section: Discussionmentioning

confidence: 99%

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Unilateral Pulmonary Agenesis about a Case Revealed by an Acute Respiratory Infection in a Young Infant

Kissou

Adjaba

Tamini

et al. 2023

Case Reports in Pediatrics

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Pulmonary agenesis is a rare congenital anomaly of unknown cause, consisting of a complete absence of the lung parenchyma, bronchi, and vascularization. It may or not be associated with other malformations. The authors report a case of right pulmonary agenesis diagnosed in a four-month-old infant who had no previous pathological history and was growing well. The circumstance of discovery was respiratory distress during an infectious episode. The diagnosis was suspected on a standard chest X-ray and confirmed on a chest CT scan. There are no other associated defects. The evolution was good after antibiotic therapy. While bilateral pulmonary agenesis is incompatible with life, the unilateral form may remain unrecognized until adulthood. The prognosis depends mainly on the importance of the associated malformations.

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Section: Discussionmentioning

confidence: 99%

“…Pulmonary agenesis is a rare congenital malformation, consisting of a complete absence of the lung parenchyma, bronchi, and vascularization [1]. Although some risk factors are sometimes mentioned, the etiology of this malformation remains unknown.…”

Section: Introductionmentioning

confidence: 99%

Unilateral Pulmonary Agenesis about a Case Revealed by an Acute Respiratory Infection in a Young Infant

Kissou

Adjaba

Tamini

et al. 2023

Case Reports in Pediatrics

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“…Chest CT remains the most specific exam to establish the diagnosis and the topography. The left upper lobe is most often affected (43%), followed by involvement of the right middle lobe (32%) and the right upper lobe (21%) [ 17 ]. The lower lobes are rarely affected, with less than 1%.…”

Section: Discussionmentioning

confidence: 99%

“…The lower lobes are rarely affected, with less than 1%. Furthermore, a few cases of bilateral ELG have been described in the literature but this remains rare [ 17 ].…”

Section: Discussionmentioning

confidence: 99%

“…The MRI with three-dimensional and vascular sequences is the alternative choice without the injection of contrast product. It helps to diagnose the malformations with a vascular component [ 17 ]. In certain atypical cases, bronchoscopy is indicated to eliminate the presence of an intrabronchial foreign body, or a mucous plug or to look for a bronchial anomaly that could be responsible for emphysema.…”

Section: Discussionmentioning

confidence: 99%

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Congenital Lobar Emphysema in Children: Case Series

Benbouziane,

Larda,

Pongo

et al. 2023

Cureus

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Recurrent wheezing is very common in infants. When these symptoms appear early without a free interval, a pulmonary malformation should be investigated. Congenital lobar emphysema is a rare abnormality of the lower respiratory tract. Here, we report a case series of six cases of congenital lobar emphysema between 2015 and 2023. Clinical and radiological data were collected according to an operating sheet previously established in our pediatric pneumo-allergology unit. They all had recurrent wheezing and dyspnea. Chest radiography and chest CT were consistent with the diagnosis of congenital lobar emphysema. All patients had lobectomy without complications.

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Congenital pulmonary airway malformations: state-of-the-art review for pediatrician’s use

et al. 2017

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Surgery remains the cornerstone treatment of symptomatic lesions but the postnatal management of asymptomatic CPAM remains controversial. There are pros and cons of surgical resection, as increasing rate of infections over time renders the surgery more difficult after months or years of evolution, as well as risk of malignancy, though exact incidence is still unknown. What is known: • Congenital pulmonary airway malformations (CPAM) are rare developmental lung malformations mainly antenatally diagnosed. • While the neonatal management of symptomatic CPAM is clear and includes prompt surgery, controversies remain for asymptomatic CPAM due to risk of infections and malignancies. What is new: • Increased rate of infection over time renders the surgery more difficult after months or years of evolution and pushes for recommendation of early elective surgery. • New molecular or pathological pathways may help in the distinction of type 4 CPAM from type I pleuropulmonary blastoma.

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Malformations pulmonaires congénitales, le point de vue du radiologue

Cited by 9 publications

References 51 publications

Unilateral Pulmonary Agenesis about a Case Revealed by an Acute Respiratory Infection in a Young Infant

Unilateral Pulmonary Agenesis about a Case Revealed by an Acute Respiratory Infection in a Young Infant

Congenital Lobar Emphysema in Children: Case Series

Congenital pulmonary airway malformations: state-of-the-art review for pediatrician’s use

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