To determine the presentation, pathologic features, treatment outcome, and prognosis of mucoepidermoid carcinoma of the parotid gland in children. Design: Retrospective clinical and histopathologic study with institutional review board approval. Setting: Tertiary pediatric medical center. Patients: Seven children (4 girls and 3 boys) presented with mucoepidermoid carcinoma of the parotid gland between 1994 and 2004. Main Outcome Measures: Clinical presentation, pathologic features, treatment outcome, complications, local recurrence, distant metastasis, and overall survival. Results: All patients presented with an asymptomatic parotid mass. Initial treatment in 7 patients included total parotidectomy (n = 3), superficial parotidectomy (n=3), transoral enucleation (n = 1), and supraomohyoid neck dissection (n=1). Four patients required additional sur